Mokhoa oa ho phekola lipodystrophy ea tlhaho ea tlhaho

Litaba

• Matšoao a congenital lipodystrophy e akaretsang
• Tlhatlhobo ea tlhaho e tsoaloang ea lipodystrophy

Kalafo ea congenital lipodystrophy, e leng lefu la liphatsa tsa lefutso le sa lumelleng ho bokellana ha mafura ka tlasa letlalo le lebisang ho bokellaneng ha eona lithong kapa mesifa, e ikemiselitse ho fokotsa matšoao, ka hona, e fapana maemong ohle. Leha ho le joalo, boholo ba nako e etsoa ka:

• Lijo tsa lik'habohaedreite, joalo ka bohobe, raese kapa litapole: e thusa ho boloka maemo a matla 'meleng a fokotsehang ka lebaka la khaello ea mafura, e lumellang kholo le kholo e tloaelehileng;
• Lijo tse mafura a fokolang: E thusa ho thibela ho bokellana ha mafura mesifeng le lithong tse joalo ka sebete kapa manyeme. Mona ke seo u lokelang ho se qoba: Lijo tse nang le mafura a mangata.
• Phekolo ea Leptin: meriana, e kang Myalept, e sebelisetsoa ho nkela hormone e hlahisoang ke lisele tse mafura, e thusang ho thibela ho qala ha lefu la tsoekere kapa maemo a phahameng a triglycerides.

Ntle le moo, kalafo e kanna ea kenyelletsa tšebeliso ea meriana ea lefu la tsoekere kapa la sebete, haeba mathata ana a se a bile teng.

Maemong a mabe ka ho fetesisa, moo ho tsoaloang ka tlhaho lipodystrophy ho bakang tšenyo e rarahaneng ea sebete kapa liphetoho sefahlehong, ho buuoa ho ka sebelisoa ho lokisa botle ba sefahleho, ho tlosa liso tsa sebete kapa, maemong a tsoetseng pele ho feta, ho kenyelletsa. ea sebete.

Matšoao a congenital lipodystrophy e akaretsang

Matšoao a congenital lipodystrophy, eo hape a tsejoang e le Berardinelli-seip Syndrome, hangata a hlaha nakong ea bongoana mme a tšoauoa ka ho haelloa ke mafura a 'mele a fanang ka ponahalo ea mesifa le methapo e hlahelletseng. Ntle le moo, ngoana a kanna a bonts'a kholo e potlakileng haholo, e lebisang ho nts'etsopele ea matsoho, maoto kapa mehlahare e meholo haholo bakeng sa lilemo tsa bona.

Ho theosa le lilemo, haeba congenital lipodystrophy e sa alafshoe ka nepo, e ka baka ho bokellana ha mafura mesifa kapa litho, ho lebisang liphellong tse kang:

• Matšoao a maholo haholo le a tsoetseng pele;
• Tšenyo e matla ea sebete;
• Mofuta oa 2 oa lefu la tsoekere;
• Ho tenya ha mesifa ea pelo;
• Maemo a phahameng a triglycerides maling;
• Boholo ba spleen.

Ntle le mathata ana, kakaretso ea congenital lipodystrophy le eona e ka baka nts'etsopele ea acanthosis nigricans, bothata ba letlalo bo lebisang ho nts'etsopele ea mabala a lefifi le a teteaneng letlalong, haholoholo molaleng, sephakeng le sebeng. Ithute haholoanyane ho: Mokhoa oa ho phekola acanthosis nigricans.

Tlhatlhobo ea tlhaho e tsoaloang ea lipodystrophy

Ho hlahlojoa ha liphatsa tsa lefutso tsa tlhaho e tloaelehileng hangata ho etsoa ke ngaka e akaretsang kapa endocrinologist, ka ho bona matšoao kapa ho lekola nalane ea mokuli, haholoholo haeba mokuli a le mosesaane haholo empa a na le mathata a kang lefu la tsoekere, triglycerides e phahameng, tšenyo ea sebete kapa acanthosis nigricans, bakeng sa mohlala.

Ntle le moo, ngaka e kanna ea laela liteko tse ling tsa tlhahlobo ea mali tse kang liteko tsa mali kapa li-MRIs, ho lekola lipid tsa mali kapa ho senngoa ha lisele tse mafura 'meleng, mohlala. Maemong a sa tloaelehang haholo, ho ka etsoa tlhahlobo ea liphatsa tsa lefutso ho bona hore na ho na le phetoho liphatseng tse itseng tse bakang congenital lipodystrophy.

Haeba ho netefatsoa hore phumano ea gengenital lipodystrophy e akaretsang, tlhabollo ea lefutso e lokela ho fanoa pele e ka ba moimana, mohlala, kaha ho na le kotsi ea ho fetisetsa lefu lena baneng.