Bartter's syndrome: ke eng, matšoao a mantlha le kalafo
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Litaba
Bartter's syndrome ke lefu le sa tloaelehang le amang liphio mme le baka tahlehelo ea potasiamo, sodium le chlorine morotong. Lefu lena le fokotsa khatello ea khalsiamo maling mme le eketsa tlhahiso ea aldosterone le renin, lihormone tse amehang taolong ea khatello ea mali.
Sesosa sa Bartter's Syndrome ke liphatsa tsa lefutso ebile ke boloetse bo fetelang ho tloha ho batsoali ho ea ho bana, bo amang batho ho tloha bongoaneng. Lefu lena ha le na pheko, empa haeba le fumanoa kapele, le ka laoloa ka meriana le litlatsetso tsa diminerale.
![](https://a.svetzdravlja.org/healths/sndrome-de-bartter-o-que-principais-sintomas-e-tratamento.webp)
Matšoao a mantlha
Matšoao a Bartter's Syndrome a hlaha bongoaneng, 'me a mantlha ke:
- Khaello ea phepo e nepahetseng;
- Kholofalo ea kholo;
- Bofokoli ba mesifa;
- Kholofalo ea kelello;
- Ho eketsa molumo oa moroto;
- Ho nyoreloa haholo;
- Ho felloa ke metsi 'meleng;
- Feberu;
- Letšollo kapa ho hlatsa.
Batho ba nang le Bartter's Syndrome ba na le potasiamo, chlorine, sodium le calcium tse ngata maling a bona, empa ha ba na liphetoho maemong a khatello ea mali. Batho ba bang ba kanna ba ba le litšobotsi tsa 'mele tse bontšang lefu lena, joalo ka sefahleho se likhutlo li tharo, phatla e hlahelletseng, mahlo a maholo le litsebe tse shebileng pele.
Tlhatlhobo ea Bartter's Syndrome e etsoa ke ngaka ea methapo ea mafu, ka ho lekola matšoao a mokuli le liteko tsa mali tse fumanang maemo a sa nepahalang poteng le lihormon tse kang aldosterone le renin.
Kalafo e etsoa joang
Kalafo ea Bartter's Syndrome e etsoa ka ts'ebeliso ea litlatsetso tsa potasiamo kapa liminerale tse ling, joalo ka magnesium kapa calcium, ho eketsa mohopolo oa lintho tsena maling, le ho noa maro a mangata, ho lefella tahlehelo e kholo ea metsi ka moroto.
Litlhare tsa diuretic tse bolokang potasiamo, joalo ka spironolactone, le tsona li sebelisoa kalafong ea lefu lena, hammoho le lithethefatsi tse seng li-steroidal tse khahlanong le ho ruruha joalo ka indomethacin, e lokelang ho nkuoa ho fihlela qetellong ea kholo ho thusa kholo ea motho .
Bakuli ba lokela ho etsa liteko tsa ultrasound tsa moroto, mali le liphio. Sena se sebeletsa ho lekola ts'ebetso ea liphio le pampiri ea meno, ho thibela litlamorao tsa kalafo ho litho tsena.