Fibrous dysplasia

Fibrous dysplasia ke lefu la masapo le senyang le ho nka sebaka sa masapo a tloaelehileng ka masapo a masapo. Lesapo le le leng kapa a mang a ka ameha.

Fibrous dysplasia hangata e hlaha bongoaneng. Batho ba bangata ba na le matšoao ha ba le lilemo li 30. Lefu lena le hlaha khafetsa ho basali.

Fibrous dysplasia e hokahane le bothata ba liphatsa tsa lefutso (gene mutation) tse laolang lisele tse hlahisang masapo. Phetoho e etsahala ha lesea le ntse le hola ka popelong. Boemo ha bo fetisoe ho tloha ho motsoali ho ea ho ngoana.

Matšoao a ka kenyelletsa efe kapa efe ea tse latelang:

• Bohloko ba masapo
• Lisosa tsa masapo
• Mathata a tšoelesa ea endocrine (hormone)
• Ho robeha kapa ho holofala ha masapo
• Mmala o sa tloaelehang oa letlalo (pigmentation), o hlahang ka McCune-Albright syndrome

Lisosa tsa masapo li ka emisa ha ngoana a kena bohlankaneng.

Mofani oa tlhokomelo ea bophelo o tla etsa tlhahlobo ea 'mele. X-ray ea masapo e nkuoa. Ho ka buelloa ka MRI.

Ha ho na pheko bakeng sa fibrous dysplasia. Ho robeha ha masapo kapa ho holofala ho alafshoa ha ho hlokahala. Mathata a hormone a tla hloka ho phekoloa.

Ponahalo e latela ho teba ha boemo le matšoao a etsahalang.

Ho ipapisitse le masapo a amehileng, mathata a bophelo bo botle a ka hlahang a kenyelletsa:

• Haeba lesapo la lehata le amehile, ho ka ba le pono kapa tahlehelo ea kutlo
• Haeba lesapo la leoto le amehile, ho ka ba le bothata ba ho tsamaea le mathata a kopaneng a kang ramatiki

Bitsa mofani oa hau haeba ngoana oa hau a e-na le matšoao a boemo bona, joalo ka ho robeha masapo khafetsa le ho holofala ha masapo ho sa hlaloseheng.

Litsebi tsa lingaka tsa masapo, endocrinology, le liphatsa tsa lefutso li ka 'na tsa ameha ho fumanoeng le tlhokomelo ea ngoana oa hau.

Ha ho na mokhoa o tsebahalang oa ho thibela fibrous dysplasia. Kalafo e ikemiselitse ho thibela mathata, joalo ka ho robeha ha masapo khafetsa, ho thusa ho etsa hore boemo bo be boima haholo.

Ho ruruha ha fibrous hyperplasia; Fibrous hyperplasia ea idiopathic; Lefu la McCune-Albright

• Anterior skeletal anatomy

Czerniak B. Fibrous dysplasia le liso tse amanang le eona. Ka: Czerniak B, ed. Lihlahala tsa Bone tsa Dorfman le Czerniak. Lekhetlo la bobeli. Philadelphia, PA: Elsevier Saunders; 2016: khaolo ea 8.

Heck RK, PC ea ho bapala. Lihlahala tsa masapo a Benign le maemo a sa sebetseng a tšoanang le lihlahala tsa masapo. Ka: Azar FM, Beaty JH, Kanale ST, eds. Masapo a sebetsang a Campbell. 13th ed. Philadelphia, PA: Elsevier; 2017: khaolo ea 25.

Mohoebi SN, Nadol JB. Lipontšo tsa Otologic tsa lefu la systemic. Ka: Flint PW, Haughey BH, Lund V, et al, eds. Cummings Otolaryngology: Ho Buuoa Hlooho le Nko. La 6th. Philadelphia, PA: Elsevier Saunders; 2015: khaolo ea 149.

Shiflett JM, Perez AJ, Motsoali AD. Likokoana-hloko tsa lehata ho bana: li-dermoids, langerhans cell histiocytosis, fibrous dysplasia le lipomas. Ka: Winn HR, e hlophisitsoeng. Phekolo ea Youmans le Winn Neurological. La 7th. Philadelphia, PA: Elsevier; 2017: khaolo ea 219.