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Phokolo ea mali e bakoang ke lithethefatsi e bakoang ke lithethefatsi ke lefu la mali le etsahalang ha moriana o hlohleletsa sesole sa 'mele ho itšireletsa lisele tsa ona tse khubelu tsa mali. Sena se etsa hore lisele tse khubelu tsa mali li senyehe pele ho nako e tloaelehileng, ts'ebetso e bitsoang hemolysis.

Phokolo ea mali ke boemo boo 'mele o se nang lisele tse khubelu tsa mali tse phetseng hantle. Lisele tse khubelu tsa mali li fana ka oksijene lithong tsa 'mele.

Ka tloaelo, lisele tse khubelu tsa mali li nka matsatsi a ka bang 120 'meleng. Haemolytic anemia, lisele tse khubelu tsa mali li senyeha pejana ho tloaelehileng.

Maemong a mang, sethethefatsi se ka etsa hore sesole sa 'mele se etse phoso lisele tsa hao tse khubelu tsa mali bakeng sa lintho tse ling. 'Mele o arabela ka ho etsa lithibela-mafu ho hlasela lisele tse khubelu tsa mali tsa' mele. Masole a mmele a hokellana le disele tse kgubedu tsa madi mme a etsa hore a senyehe kapele haholo.

Lithethefatsi tse ka bakang mofuta ona oa phokolo ea mali ea hemolytic li kenyelletsa:

  • Cephalosporins (sehlopha sa lithibela-mafu), sesosa se tloaelehileng haholo
  • Dapsone
  • Levodopa
  • Levofloxacin
  • Methyldopa
  • Nitrofurantoin
  • Lithethefatsi tse seng khahlanong le ho ruruha (li-NSAID)
  • Penicillin le lihlahisoa tsa eona
  • Phenazopyridine (pyridium)
  • Quinidine

Mofuta o sa tloaelehang oa lefu lena ke phokolo ea mali ea hemolytic e tsoang khaellong ea tsoekere-6 phosphate dehydrogenase (G6PD). Tabeng ena, ho senyeha ha lisele tse khubelu tsa mali ho bakoa ke mofuta o itseng oa khatello ea maikutlo ka seleng.


Phokolo ea mali e bakoang ke lithethefatsi ha e fumanehe hangata ho bana.

Matšoao a ka kenyelletsa efe kapa efe ea tse latelang:

  • Moroto o lefifi
  • Mokhathala
  • 'Mala oa letlalo o phatsimang
  • Ho otla ha pelo ka potlako
  • Phefumoloho e khutšoanyane
  • Letlalo le mosehla le makhooa a mahlo (jaundice)

Tlhahlobo ea 'mele e ka bonts'a spleen e holisitsoeng. U kanna oa ba le liteko tsa mali le moroto ho thusa ho fumana boemo bona.

Liteko li ka kenyelletsa:

  • Palo ea li-reticulocyte ka botlalo ho fumana hore na lisele tse khubelu tsa mali li ntse li etsoa mongoaneng oa masapo ka sekhahla se loketseng
  • Teko ea Coombs e tobileng kapa e sa tobang ho netefatsa hore na ho na le lisireletsi tse khahlano le lisele tse khubelu tsa mali tse etsang hore lisele tse khubelu tsa mali li shoe kapele haholo
  • Methati e sa tobang ea bilirubin ho lekola jaundice
  • Palo e khubelu ea lisele tsa mali
  • Serum haptoglobin ho netefatsa hore na lisele tse khubelu tsa mali li senyeha kapele haholo
  • Urogogin ea moroto ho hlahloba hemolysis

Ho emisa sethethefatsi se bakang bothata ho ka imolla kapa sa laola matšoao.


U kanna ua hloka ho noa moriana o bitsoang prednisone ho hatella boits'ireletso ba mmele khahlanong le lisele tse khubelu tsa mali. Litšelo tse khethehileng tsa mali li ka hlokahala ho phekola matšoao a matla.

Phello e ntle ho batho ba bangata haeba ba khaotsa ho noa moriana o bakang bothata.

Lefu le bakoang ke khaello ea mali e matla ke seoelo.

Bona mofani oa tlhokomelo ea bophelo haeba u na le matšoao a boemo bona.

Qoba sethethefatsi se bakileng boemo bona.

Immune hemolytic anemia ho latela lithethefatsi; Anemia - immune hemolytic - kamora lithethefatsi

  • Masole a mmele

Michel M. Autoimmune le li-intravascular hemolytic anemias. Ka: Goldman L, Schafer AI, li-eds. Phekolo ea Goldman-Cecil. La 25th ed. Philadelphia, PA: Elsevier Saunders; 2016: khaolo ea 160.

Hlōla N, Richards SJ. E fumanoeng ke haemolytic anaemias. Ka: Bain BJ, Bates I, Laffan MA, eds. Dacie le Lewis e sebetsang Hematology. 12th ed. Philadelphia, PA: Elsevier; 2017: khaolo ea 13.


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