IgA vasculitis - Henoch-Schönlein purpura

IgA vasculitis ke lefu le kenyang mabala a pherese letlalong, bohloko ba manonyeletso, mathata a mala le glomerulonephritis (mofuta oa lefu la liphio). E boetse e tsejoa e le Henoch-Schönlein purpura (HSP).

IgA vasculitis e bakoa ke karabelo e sa tloaelehang ea sesole sa 'mele. Phello ke ho ruruha methapong e menyenyane ea mali letlalong. Methapo ea mali manonyellong, liphio kapa mala le eona e ka ameha. Ha ho hlake hore na hobaneng sena se etsahala.

Lefu lena le bonahala haholo ho bana ba pakeng tsa lilemo tse 3 le 15, empa le ka bonoa le ho batho ba baholo. E atile haholo ho bashemane ho feta banana. Batho ba bangata ba hlahisang lefu lena ba na le tšoaetso e phahameng ea ho hema libekeng tse fetileng.

Matšoao le likarolo tsa IgA vasculitis li ka kenyelletsa:

• Matheba a maputsoa letlalong (purpura). Sena se etsahala hoo e batlang e le bana bohle ba nang le boemo bona. Hangata hona ho hlaha holim'a marako, maoto a tlase le litsoeng.
• Bohloko ba mpeng.
• Bohloko bo kopaneng.
• Moroto o sa tloaelehang (o kanna oa se be le matšoao).
• Letšollo, ka linako tse ling le na le mali.
• Hives kapa angioedema.
• Ho nyekeloa le ho hlatsa.
• Ho ruruha le bohloko botlaaseng ba bashanyana.
• Ho opeloa ke hlooho.

Mofani oa tlhokomelo ea bophelo o tla sheba 'mele oa hau mme a shebe letlalo la hao. Tlhahlobo ea 'mele e tla bontša liso tsa letlalo (purpura, liso) le bonolo bo kopaneng.

Liteko li ka kenyelletsa:

• Urinalysis e lokela ho etsoa maemong ohle.
• Palo e felletseng ea mali. Platelet e kanna ea ba e tloaelehileng.
• Liteko tsa coagulation: tsena e lokela ho ba tse tloaelehileng.
• Letlalo biopsy, haholo-holo ho batho ba baholo.
• Liteko tsa mali ho batla lisosa tse ling tsa ho ruruha ha methapo ea mali, joalo ka systemic lupus erythematosus, vasculitis e amanang le ANCA kapa hepatitis.
• Ho batho ba baholo, biopsy ea liphio e lokela ho etsoa.
• Ho nahana ka liteko tsa mpa haeba bohloko bo le teng.

Ha ho na kalafo e khethehileng. Maemo a mangata a ea a le mong. Mahlaba a kopaneng a ka ntlafala le li-NSAID tse kang naproxen. Haeba matšoao a sa fele, o ka fuoa meriana ea corticosteroid e kang prednisone.

Hangata lefu lena le ba betere ka bolona. Karolo ea bobeli borarong ea bana ba nang le IgA vasculitis ba na le sekhetho se le seng feela. Karolo ea boraro ea bana e na le mananeo a mangata. Batho ba lokela ho ba le tlhaiso-leseling e haufi ea bongaka ka likhoeli tse 6 kamora liketsahalo ho batla matšoao a lefu la liphio. Batho ba baholo ba na le kotsi e kholo ea ho tšoaroa ke lefu le sa foleng la liphio.

Mathata a ka kenyelletsa:

• Ho tsoa mali kahare ho mmele
• Ho thibela mala (ho bana)
  
• Mathata a liphio (maemong a sa tloaelehang)

Bitsa mofani oa hau haeba:

• U ba le matšoao a IgA vasculitis, 'me e nka nako e fetang matsatsi a' maloa.
• U na le moroto o mebala kapa tlhahiso e tlase ea moroto kamora ketsahalo.

Immunoglobulin A vasculitis; Leukocytoclastic vasculitis; Henoch-Schönlein purpura; HSP

• Henoch-Schonlein purpura maotong a tlase
• Henoch-Schonlein purpura
• Henoch-Schonlein purpura
• Henoch-Schonlein purpura
• Henoch-Schonlein purpura ka leoto la lesea
• Henoch-Schonlein purpura maotong a lesea
• Henoch-Schonlein purpura maotong a lesea
• Henoch-Schonlein purpura maotong

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Sunderkötter CH, Zelger B, Chen KR, le al. Nomenclature ea li-vasculitis tse sehiloeng: Dermatologic addendum ho Seboka sa Machaba sa Tumellano ea Tumellano ea Machaba sa Chapel sa 2012. Ramatiki Rheumatol. 2018; 70 (2): 171-184. PMID: 29136340 www.ncbi.nlm.nih.gov/pubmed/29136340.