Lefu la Wiskott-Aldrich

Litaba

• Matšoao a Wiskott-Aldrich Syndrome
• Kalafo ea Wiskott-Aldrich Syndrome

Wiskott-Aldrich syndrome ke lefu la lefutso, le fokolisang sesole sa 'mele se amang li-lymphocyte tsa T le B, le lisele tsa mali tse thusang ho laola ho tsoa mali, liplatelete.

Matšoao a Wiskott-Aldrich Syndrome

Matšoao a wiskott-Aldrich syndrome e ka ba:

Tloaelo ea ho tsoa mali:

• Palo e fokotsehileng le boholo ba liplatelete maling;
• Ho tsoa mali hanyane ka hanyane ho khetholloang ka matheba a maputsoa a boputsoa bo boholo ba hlooho ea phini, e bitsoang "petechiae", kapa e kanna ea ba kholo ebile e tšoana le matetetso;
• Litulo tse nang le mali (haholo bongoaneng), marenene a tsoang mali le nosebleeds ea nako e telele.

Khafetsa tšoaetso e bakoang ke mefuta eohle ea likokoana-hloko tse kang:

• Otitis media, sinusitis, pneumonia;
• Meningitis, pneumonia e bakoang ke Pneumocystis jiroveci;
• Tšoaetso ea letlalo la kokoana-hloko e bakoang ke molluscum contagiosum.

Eczema:

• Khafetsa tšoaetso ea letlalo;
• Matheba a lefifi letlalong.

Lipontšo tsa autoimmune:

• Vasculitis;
• Khaello ea mali hemolytic;
• Idiopathic thrombocytopenic purpura.

Ho fumanoa ha lefu lena ho ka etsoa ke ngaka ea bana kamora ho hlokomela matšoao le liteko tse ikhethang. Ho lekola boholo ba liplatelete ke e 'ngoe ea litsela tsa ho fumana lefu lena, hobane ke mafu a fokolang a nang le tšobotsi ena.

Kalafo ea Wiskott-Aldrich Syndrome

Kalafo e nepahetseng ka ho fetisisa bakeng sa lefu la Wiskott-Aldrich ke ho kenyelletsa 'moko oa masapo. Mefuta e meng ea kalafo ke ho tlosoa ha spleen, kaha setho sena se senya liplatelete tse nyane tseo batho ba nang le lefu lena ba nang le tsona, ts'ebeliso ea hemoglobin le ts'ebeliso ea lithibela-mafu.

Tšepo ea bophelo ea batho ba nang le lefu lena e tlase, ba pholohang kamora lilemo tse leshome hangata ba ba le lihlahala tse kang lymphoma le leukemia.