Lefu la Fanconi

Litaba

• Matšoao a Fanconi Syndrome
• Kalafo ea Fanconi Syndrome
• Lihokelo tse sebetsang:

Fanconi syndrome ke lefu le sa tloaelehang la liphio le lebisang ho bokellaneng ha tsoekere, bicarbonate, potasiamo, phosphates le li-amino acid tse ngata tse feteletseng morotong. Lefu lena le boetse le na le tahlehelo ea protheine morong 'me moroto o ba matla le ho ba asiti.

Hereditary Fanconi Syndrome e baka liphetoho tsa lefutso tse fetisoang ho tloha ho ntate ho ea ho mora. Ebang Lefu la Fanconi le fumanoeng, ho kenella ka lirafshoa tse boima, joalo ka loto, ho kenella ha lithibela-mafu tse seng li felile, ho haella ha vithamine D, ho kenya liphio, multipleeloma kapa amyloidosis ho ka lebisa ho nts'etsopele ea lefu lena.

Fanconi Syndrome ha e na pheko mme kalafo ea eona e na le ho tlosa lintho tse lahlehileng morotong, tse bontšitsoeng ke nephrologist.

Matšoao a Fanconi Syndrome

Matšoao a Fanconi Syndrome e ka ba:

• Ho ntša metsi a mangata haholo;
• Moroto o matla le o nang le asiti;
• Ho nyoreloa haholo;
• Ho felloa ke metsi 'meleng;
• Nakoana;
• Acid e phahameng maling;
• Bofokoli;
• Bohloko ba masapo;
• Matheba a 'mala oa kofi letlalong;
• Ho ba sieo kapa sekoli menoaneng e metona ea maoto;

Ka kakaretso, semelo sa Fanconi Syndrome lefa le hlaha bongoaneng lilemong tse ka bang 5.

O tlhahlobo ea Fanconi Syndrome e etsoa ho ipapisitsoe le matšoao, tlhahlobo ea mali e senolang acidity e phahameng le teko ea moroto e bonts'ang tsoekere e fetelletseng, phosphate, bicarbonate, uric acid, potasiamo le sodium.

Kalafo ea Fanconi Syndrome

Kalafo ea Fanconi Syndrome e ikemiselitse ho tlatselletsa lintho tse lahliloeng ke batho ba moroto. Bakeng sa sena, ho ka hlokahala hore bakuli ba noe potasiamo, phosphate le vithamine D tlatsetso, hammoho le sodium bicarbonate ho fokotsa acidosis ea mali.

Bakeng sa bakuli ba nang le ts'oaetso e matla ea liphio, ho fetisoa ha liphio ho bontšoa.

Lihokelo tse sebetsang:

• Lijo tse nang le potassium
• Lijo tse nang le vithamine D e ngata

• Ho fetisetsa liphio