Osteopetrosis: ke eng, matšoao le kalafo

Litaba

• Matšoao a Osteopetrosis
• Lisosa tsa osteopetrosis
• Kalafo e etsoa joang

Osteopetrosis ke lefu le sa tloaelehang le futsitseng lefu la masapo leo masapo a leng boima ho feta a tloaelehileng, a etsahalang ka lebaka la ho se leka-lekane ha lisele tse ikarabellang molemong oa ho theoa ha masapo le ho robeha, ho ts'ehetsa keketseho e akaretsang ea masapo le ho baka matšoao a joalo ka masapo a robehileng, ho utloa ka thata le liphetoho ho nts'etsopele ea methapo ea kutlo, mohlala.

Kalafo ea osteopetrosis e lokela ho khothaletsoa ke sehlopha sa bongaka se kenyeletsang ngaka ea bana, hematologist le orthopedist, mme phetisetso ea moko oa masapo hangata e khothaletsoa molemong oa ho ntlafatsa ts'ebetso ea lisele tse amanang le sebopeho sa masapo.

Matšoao a Osteopetrosis

Matšoao a osteopetrosis a ka tsejoa nakoana kamora ho hlaha, kaha ke lefu la tlhaho, kapa ho ka ba le matšoao le ha a se a le moholo. Tšobotsi e ka sehloohong ea osteopetrosis ke keketseho ea bongata ba masapo, bo ka bonoang ka ho lekola densitometry ea masapo.

Ho phaella moo, ho boetse ho na le menyetla e kholo ea ho robeha, hobane ka lebaka la ho senyeha ha lisele tse ikarabellang bakeng sa ts'ebetso ea ho thehoa ha masapo le ho senyeha, masapo a senyeha haholoanyane.

Matšoao a osteopetrosis a amana le taba ea hore ho na le ponahalo e kholo ea masapo 'meleng, e ka lebisang liphetohong' meleng, matšoao a mantlha ke:

• Pono e lerootho;
• Bothata ba kutlo;
• Matšoao a iphetang a meno le marenene;
• Ho eketsa sebete le spleen, ho fella ka tlhahiso e fetotsoeng ea lisele tsa mali;
• Phetoho kholisong ea methapo ea kutlo;
• Ho lieha ho hlaha ha meno;
• Khatello e eketsehileng ea khatello ea kelello.

Ho fumanoa ha osteopetrosis ho entsoe ke ngaka ea masapo ka ho etsa liteko tsa litšoantšo tse kang X-ray le bone densitometry, e leng tlhahlobo e bonolo le e se nang bohloko e ikemiselitseng ho netefatsa botenya ba masapo a motho, ka mohlala. Utloisisa hore na osteopetrosis ke eng le hore na e etsoa joang.

Leha ho le joalo, ho netefatsa mofuta le mathata a osteopetrosis, ngaka e kanna ea odara liteko tse ling tsa tlhahlobo, joalo ka computed tomography kapa imagin resonance imaging ho lekola boteng ba liso lithong tse ling tse kang mahlo le litsebe, ntle le liteko tsa mali.

Lisosa tsa osteopetrosis

Osteopetrosis e bakoa ke liphoso tsa lefutso le le leng kapa ho feta tse ikarabellang bakeng sa ho theoa le nts'etsopele ea li-osteoclast, e leng lisele tse ntšang masapo a khale a masapo ebe li li nkela sebaka se secha se phetseng hantle. Ho ipapisitse le tšimoloho ea liphatsa tsa lefutso tse fetotsoeng, mofuta oa osteopetrosis o ka fapana:

• Malignant bongoaneng osteopetrosis: ngoana o na le lefu lena ho tloha ha a hlaha ka lebaka la bokooa liphatseng tsa lefutso tse tsoang ho ntate le mme;
• Motho e moholo osteopetrosis: osteopetrosis e fumanoa feela nakong ea bocha kapa ho ba motho e moholo, e bakoa ke liphatsa tsa lefutso tse fetotsoeng ho tsoa ho ntate kapa mme feela.

Tabeng ea motho e moholo ea bitsoang osteopetrosis, phetoho ea liphatsa tsa lefutso le eona e ka bakoa ke phetoho, ntle le hore e ka rua phetoho ea batsoali.

Kalafo e etsoa joang

Kalafo ea osteopetrosis e tlameha ho tataisoa ke sehlopha sa litsebi tse 'maloa tsa bophelo bo botle, joalo ka ngaka ea bana, ngaka ea masapo, hematologist, endocrinologist le physiotherapist.

Hajoale, kalafo e sebetsang ka ho fetesisa bakeng sa osteopetrosis ke ho kenyelletsa 'moko oa masapo, kaha lisele tse laoloang molaong li hlahisoa lenaneng leo. Kahoo, ha u kenya motho setala, ho a khonahala ho laola tšebetso ea lisele tse ikarabellang bakeng sa ho theoa le ho senyeha ha masapo, ho loantša osteopetrosis. Utloisisa hore na phetisetso ea moko oa masapo e etsoa joang.

Le ha phetisetso ea moko oa masapo e le kalafo e khothalelitsoeng ea ho folisa lefu lena, kalafo tse ling li ka buelloa ho ts'ehetsa phomolo ea matšoao, joalo ka:

• Liente tse nang le Interferon gamma-1b, e leng sethethefatsi se khonang ho liehisa nts'etsopele ea lefu lena;
• Tšebeliso ea Calcitriol, e leng mofuta o sebetsang oa vithamine D o thusang ho hlasimolla lisele tsa masapo ho hola ka mokhoa o tloaelehileng le ho fokotsa masapo a masapo;
• Ho kenngoa ha Prednisone, e leng hormone e tšoanang le cortisone e ka ntlafatsang tlhahiso ea lisele tsa tšireletso 'meleng, tse hlahisoang masapong;
• Physiotherapy mananeo, kaha li ntlafatsa matla a 'mele a mokuli, li thusa ho thibela ho robeha ha masapo le ho ntlafatsa boipuso mesebetsing e meng ea letsatsi le letsatsi.

Ngaka e kanna ea u eletsa hore u buisane le setsebi sa phepo e nepahetseng hore u fetole tsela eo u jang ka eona ho kenyelletsa lijo tse thusang ho nts'etsapele kholo ea 'mele le masapo, haholoholo bongoaneng.

Ntle le moo, ho bohlokoa ho etela ngaka ea mahlo ka mehla, otolaryngologist le ngaka ea meno ho lekola nts'etsopele le ponahalo e ka bang teng ea liso kapa bofokoli mahlong, meno, nko, litsebe le 'metso, mohlala.