Sengoli: Gregory Harris
Letsatsi La Creation: 8 April 2021
Ntlafatsa Letsatsi: 16 Mots’Eanong 2024
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Matšoafo dystrophy - Moriana
Matšoafo dystrophy - Moriana

Li-fuchs (tse bitsoang "fooks") dystrophy ke lefu la mahlo leo ho lona lisele tse koahelang bokahare ba cornea li qalang ho shoa butle. Lefu lena hangata le ama mahlo ka bobeli.

Fuchs dystrophy e ka futsetsoa, ​​ho bolelang hore e ka fetisoa ho tloha ho batsoali ho ea ho bana. Haeba e mong oa batsoali ba hau a na le lefu lena, o na le monyetla oa 50% oa ho ba le boemo bona.

Leha ho le joalo, boemo bona bo kanna ba hlaha ho batho ba se nang nalane ea lelapa e tsebahalang ea lefu lena.

Fuchs dystrophy e atile haholo ho basali ho feta banna. Mathata a pono ha a hlahe pele ho lilemo tse 50 maemong a mangata. Leha ho le joalo, mofani oa tlhokomelo ea bophelo a ka khona ho bona matšoao a lefu ho batho ba anngoeng ke lilemo tse 30 kapa 40.

Fuchs dystrophy e ama lisele tse tšesaane tse ka morao ho cornea. Lisele tsena li thusa ho pompa mokelikeli o feteletseng ka ntle ho cornea. Ha lisele tse ngata li ntse li lahleha, mokelikeli o qala ho bopa cornea, e baka ho ruruha le cornea e koahetsoeng ke maru.

Qalong, mokelikeli o ka bokella feela nakong ea boroko, ha leihlo le koetsoe. Ha lefu lena le ntse le mpefala, makhopho a manyenyane a ka hlaha. Malengelena aa hola 'me a ka qetella a robehile. Sena se baka bohloko ba mahlo. Fuchs dystrophy le eona e ka etsa hore sebopeho sa cornea se fetohe, se lebisang ho mathata a mangata a pono.


Matšoao a ka kenyelletsa:

  • Bohloko ba mahlo
  • Ho utloahala ha mahlo ho khanya le ho phatsima
  • Pherekano kapa pono e lerootho, qalong feela hoseng
  • Ho bona li-halos tse mebala-bala ho pota mabone
  • Pono e ntseng e mpefala letsatsi lohle

Mofani oa thepa a ka hlahloba Fuchs dystrophy nakong ea tlhahlobo ea lebone.

Liteko tse ling tse ka etsoang li kenyelletsa:

  • Pachymetry - e lekanya botenya ba cornea
  • Tlhahlobo e ikhethileng ea microscope - e lumella mofani hore a shebe lera le lesesaane la lisele tse molaong o ka morao oa cornea
  • Teko ea mahlo a mahlo

Marotholi a mahlo kapa mafura a hulang mokelikeli ho tsoa ho cornea a sebelisetsoa ho kokobetsa matšoao a Fuchs dystrophy.

Haeba liso tse bohloko li hlaha ho cornea, lilense tse bonolo tsa ho ikopanya kapa ho buuoa ho etsa mabali holim'a lisosa ho ka thusa ho fokotsa bohloko.

Pheko feela ea Fuchs dystrophy ke ho kenyelletsa 'mele.

Ho fihlela haufinyane tjena, mofuta o atileng ka ho fetesisa oa corneal e ne e le keratoplasty e kenang. Nakong ea ts'ebetso ena, karoloana e nyane ea sekhahla e tlosoa, e siea monyako ka pel'a leihlo. Karolo e lekanang ea cornea e tsoang ho mofani oa motho e ntan'o rokelloa monyako o ka pele ho leihlo.


Mokhoa o mocha o bitsoang endothelial keratoplasty (DSEK, DSAEK, kapa DMEK) e se e le khetho e ratoang bakeng sa batho ba nang le Fuchs dystrophy. Ts'ebetsong ena, ke likarolo tse ka hare tsa cornea feela tse nkeloang sebaka, ho fapana le likarolo tsohle. Sena se lebisa ho hlaphoheloeng kapele le ho ba le mathata a fokolang. Hangata ha ho hlokahale hore motho a otlolohe.

Fuchs dystrophy e mpefala ha nako e ntse e feta. Ntle le ho kenyelletsa 'mele, motho ea nang le lefu le matla la Fuchs dystrophy a ka foufala kapa a ba le bohloko bo boholo mme a fokotsa pono.

Maemo a bonolo a Fuchs dystrophy hangata a mpefala kamora ho buuoa ka lera. Ngaka e buoang ea cataract e tla lekola kotsi ena mme e ka fetola mokhoa kapa nako ea ts'ebetso ea hau ea cataract.

Bitsa mofani oa hau haeba u na le:

  • Bohloko ba mahlo
  • Ho utloahala ha leihlo ho leseli
  • Boikutlo ba hore ho na le ho hong ka leihlong la hao ha ho se na letho moo
  • Mathata a pono joalo ka ho bona li-halos kapa pono e koahetsoeng ke maru
  • Pono e ntseng e mpefala

Ha ho na thibelo e tsebahalang. Ho qoba ho buuoa ka lera la leihlo kapa ho nka mehato e khethehileng ea ho itšireletsa nakong ea ts'ebetso ea leihlo ho ka liehisa tlhoko ea ho kenyelletsa 'mele.


Ho fokola ha 'mele ka Fuchs; Fuchs 'endothelial ho senyeha ha' mele; Fuchs 'corneal dystrophy

Folberg R. Leihlo. Ka: Kumar V, Abbas AK, Aster JC, bahlophisi. Robbins & Cotran Pathologic Motheo oa Mafu. 10th ed. Philadelphia, PA: Elsevier; 2021: khaolo ea 29.

Patel SV. Ho ea litekong tsa bongaka litabeng tsa fuchs endothelial corneal dystrophy: mekhahlelo ea liphetho le sephetho - thuto ea Bowman Club 2019. BMJ Open Ophthalmology. 2019; 4 (1): e000321. PMID: 31414054 e fetotsoe.ncbi.nlm.nih.gov/31414054/.

Rosado-Adames N, Afshari NA. Maloetse a endothelium ea corneal. Ka: Yanoff M, Duker JS, bahlophisi. Ophthalmology. La 5th. Philadelphia, PA: Elsevier; 2019: khaolo ea 4.21.

Salmone JF. Cornea. Ka: Salmon JF, e hlophisitsoeng. Kanski's Clinical Ophthalmology. La 9th. Philadelphia, PA: Elsevier; 2020: khaolo ea 7.

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