Sengoli: Clyde Lopez
Letsatsi La Creation: 23 Phupu 2021
Ntlafatsa Letsatsi: 1 Phupu 2024
Anonim
Teko ea Donath-Landsteiner - Moriana
Teko ea Donath-Landsteiner - Moriana

Teko ea Donath-Landsteiner ke teko ea mali ho fumana lithibela-mafu tse kotsi tse amanang le lefu le sa tloaelehang le bitsoang paroxysmal cold hemoglobinuria. Li-antibodies tsena li theha le ho senya lisele tse khubelu tsa mali ha 'mele o pepesehetse maemong a batang a batang.

Ho hlokahala sampole ea mali.

Ha ho litokisetso tse khethehileng tse hlokahalang.

Ha nale e kentsoe ho hula mali, batho ba bang ba utloa bohloko bo itekanetseng. Ba bang ba ikutloa feela ho hlaba kapa ho hlaba. Kamora moo, ho ka ba le ho phatloha kapa ho longoa hanyane. Haufinyane sena sea fela.

Teko ena e etsoa ho netefatsa phumano ea paroxysmal cold hemoglobinuria.

Teko e nkuoa e le tloaelo haeba ho se na li-antibodies tsa Donath-Landsteiner tse teng. Sena se bitsoa sephetho se fosahetseng.

Mekhahlelo e tloaelehileng ea boleng e ka fapana hanyane hara lilaboratori tse fapaneng. Li-lab tse ling li sebelisa litekanyo tse fapaneng kapa li leka liteko tse fapaneng. Bua le mofani oa tlhokomelo ea bophelo mabapi le moelelo oa sephetho sa hau sa liteko.

Liphetho tse sa tloaelehang li bolela hore lithibela-mafu tsa Donath-Landsteiner li teng. Sena ke pontšo ea paroxysmal batang hemoglobinuria.


Ha ho na kotsi e kholo ea ho nkuoa mali a hau. Methapo le methapo li fapana ka boholo ho tloha ho motho e mong ho ea ho o mong le ho tloha lehlakoreng le leng la 'mele ho ea ho le leng. Ho nka mali ho batho ba bang ho ka ba thata ho feta ho ba bang.

Likotsi tse ling tse amanang le ho huloa mali li nyane, empa li ka kenyelletsa:

  • Ho tsoa mali a mangata
  • Ho akheha kapa ho ikutloa o le hlooho e boima
  • Li-punctures tse ngata ho fumana methapo
  • Hematoma (mali a hahiloeng ka tlas'a letlalo)
  • Tšoaetso (kotsi e nyane neng kapa neng ha letlalo le robehile)

Lesole la mmele la anti-P; Paroxysmal batang hemoglobinuria - Donath-Landsteiner

Elghetany MT, Schexneider KI, mathata a Banki K. Erythrocytic. Ka: McPherson RA, Pincus MR, bahlophisi. Henry's Clinical Diagnosis le Tsamaiso ka Mekhoa ea Laboraro. La bo23 la ed. St Louis, MO: Elsevier; 2017: khaolo ea 32.

Michel M. Autoimmune le li-intravascular hemolytic anemias. Ka: Goldman L, Schafer AI, li-eds. Phekolo ea Goldman-Cecil. La 26th. Philadelphia, PA: Elsevier; 2020: khaolo ea 151.


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