Liteko tsa Porphyrin

Litaba

• Liteko tsa porphyrin ke life?
• Li sebelisetsoa eng?
• Hobaneng ha ke hloka tlhahlobo ea porphyrin?
• Ho etsahalang nakong ea tlhahlobo ea porphyrin?
• Na ke tla hloka ho etsa eng kapa eng ho itokisetsa tlhahlobo?
• Na ho na le likotsi tsa liteko tsa porphyrin?
• Liphetho li bolelang?
• Na ho na le eng kapa eng eo ke hlokang ho e tseba ka liteko tsa porphyrin?
• Litšupiso

Liteko tsa porphyrin ke life?

Liteko tsa Porphyrin li lekanya boemo ba li-porphyrin maling a hao, morong kapa setulong. Li-Porphyrin ke lik'hemik'hale tse thusang ho etsa hemoglobin, mofuta oa protheine liseleng tse khubelu tsa mali. Hemoglobin e tsamaisa oksijene matšoafong a hao ho ea 'meleng oohle oa hau.

Ke ntho e tloaelehileng ho ba le li-porphyrin tse nyane maling a hao le maro a mang a 'mele. Empa porphyrin e ngata e ka bolela hore o na le mofuta oa porphyria. Porphyria ke lefu le sa tloaelehang le ka bakang mathata a tebileng a bophelo bo botle. Porphyria hangata e arotsoe ka mekhahlelo e 'meli:

• Li-porphyrias tse ntle, e amang haholo tsamaiso ea methapo mme e baka matšoao a mpa
• Li-porphyrias tse fokolang, e bakang matšoao a letlalo ha u pepesehetse khanya ea letsatsi

Li-porphyrias tse ling li ama tsamaiso ea methapo le letlalo.

Mabitso a mang: protoporphyrin; protoporphyrin, mali; protoporhyrin, setuloana; li-porphyrins, mantle; uroporphyrin; li-porphyrins, moroto; Teko ea Mauzerall-Granick; asiti; ALA; porphobilinogen; PBG; protoporphyrin ea mahala ea erythrocyte; likaroloana tsa erythrocyte porphyrins; FEP

Li sebelisetsoa eng?

Liteko tsa Porphyrin li sebelisoa ho fumana kapa ho lekola porphyria.

Hobaneng ha ke hloka tlhahlobo ea porphyrin?

U kanna ua hloka tlhahlobo ea porphyrin haeba u na le matšoao a porphyria. Ho na le matšoao a fapaneng bakeng sa mefuta e fapaneng ea porphyria.

Matšoao a acute porphyria a kenyelletsa:

• Bohloko ba mpeng
• Ho sokela
• Ho nyekeloa le ho hlatsa
• Moroto o mokgubedu kapa o sootho
• Ho fokotsa kapa ho opeloa matsohong le / kapa maotong
• Bofokoli ba mesifa
• Pherekano
• Litlelase

Matšoao a porphyria ea cutaneous a kenyelletsa:

• Ho ameha haholo ka khanya ea letsatsi
• Blisters letlalong le chabetsoe ke khanya ea letsatsi
• Bofubelu le ho ruruha letlalong le pepesitsoeng
• Ho hlohlona
• Liphetoho mmala oa letlalo

U kanna ua hloka tlhahlobo ea porphyrin haeba motho e mong ka lapeng la hau a na le porphyria. Mefuta e mengata ea porphyria e futsitsoe, ho bolelang hore boemo bo fetisoa ho tloha ho motsoali ho ea ho ngoana.

Ho etsahalang nakong ea tlhahlobo ea porphyrin?

Li-porphyrin li ka hlahlojoa ka mali, moroto kapa setuloana. Mefuta e tloaelehileng ea liteko tsa porphyrin e thathamisitsoe ka tlase.

• Teko ea Mali
  • Ngaka ea tlhokomelo ea bophelo e tla nka sampole ea mali mothapong o letsohong la hao, e sebelisa nale e nyane. Kamora hore nalete e kenngoe, ho tla bokelloa mali a manyane ka har'a pompo ea liteko. U ka ikutloa u hlaba hanyane ha nale e kena kapa e tsoa. Hangata hona ho nka nako e ka tlase ho metsotso e mehlano.
• Mohlala oa Urine ea Lihora tse 24
  • U tla bokella moroto oa hau kaofela nakong ea lihora tse 24. Bakeng sa teko ena, mofani oa tlhokomelo ea bophelo kapa laboratori e tla u fa setshelo le litaelo tse ikhethang tsa hore na u ka bokella mehlala ea hau joang lapeng. Etsa bonnete ba hore u latela litaelo tsohle ka hloko. Teko ea sampole ea lihora tse 24 ea moroto e sebelisoa hobane bongata ba lintho tsa moroto, ho kenyeletsoa porphyrin, bo ka fapana ho pholletsa le letsatsi. Kahoo ho bokella mehlala e mengata ka letsatsi ho ka fana ka setšoantšo se nepahetseng haholoanyane sa lintho tsa hau tsa moroto.
• Teko e sa Lebelloang ea Moroto
  • O ka fana ka sampole ea hau nako efe kapa efe ea letsatsi, ho se litokisetso tse khethehileng kapa ts'ebetso e hlokahalang. Teko ena hangata e etsoa ofising ea mofani oa tlhokomelo ea bophelo kapa laborakeng.
• Stool Test (eo hape e bitsoang protoporphyrin ka setuloana)
  • U tla bokella mohlala oa setuloana sa hau ebe u se beha ka setsing se khethehileng. Mofani oa hao oa tlhokomelo ea bophelo o tla u fa litaelo tsa hore na u ka lokisa sampole ea hau joang le ho e romella lab.

Na ke tla hloka ho etsa eng kapa eng ho itokisetsa tlhahlobo?

Ha o hloke litokisetso tse khethehileng bakeng sa liteko tsa mali kapa tsa moroto.

Bakeng sa tlhahlobo ea setuloana, o ka laeloa hore o se ke oa ja nama kapa oa noa meriana e nang le aspirin matsatsi a mararo pele ho tlhahlobo ea hau.

Na ho na le likotsi tsa liteko tsa porphyrin?

Ho na le kotsi e nyane haholo ea ho etsa tlhahlobo ea mali. U kanna oa ba le mahlaba a fokolang kapa ho longoa moo nale e kentsoeng teng, empa matšoao a mangata a fela kapele.

Ha ho na likotsi tse tsebahalang tsa liteko tsa moroto kapa setuloana.

Liphetho li bolelang?

Haeba maemo a phahameng a porphyrin a fumanoa maling a hao, morong kapa setulong, mofani oa hao oa tlhokomelo ea bophelo o tla laela liteko tse ling ho netefatsa hore na o na le porphyria ea mofuta ofe. Le ha ho se na pheko ea porphyria, boemo bo ka laoloa. Liphetoho tse itseng tsa bophelo le / kapa meriana li ka thusa ho thibela matšoao le mathata a lefu lena. Kalafo e khethehileng e ipapisitse le mofuta oa porphyria eo u nang le eona. Haeba u na le lipotso mabapi le liphetho tsa hau kapa ka porphyria, bua le mofani oa tlhokomelo ea bophelo.

Ithute haholoanyane ka liteko tsa laboratori, libaka tsa litšupiso, le liphetho tsa kutloisiso.

Na ho na le eng kapa eng eo ke hlokang ho e tseba ka liteko tsa porphyrin?

Le ha mefuta e mengata ea porphyria e futsitsoe, mefuta e meng ea porphyria le eona e ka fumanoa. Porphyria e ka fumanoang e ka bakoa ke lintlha tse fapaneng, ho kenyeletsoa ho pepesehela lead, HIV, hepatitis C, tšebeliso e ngata ea tšepe, le / kapa ts'ebeliso e mpe ea joala.

Litšupiso

1. Mokhatlo oa American Porphyria [Internet]. Houston: Motheo oa American Porphyria; c2010–2017. Mabapi le Porphyria; [e qotsitsoeng ka la 9 Tšitoe 26]; [li-skrini tse ka bang 3]. E fumaneha ho tsoa ho: https://www.porphyriafoundation.org/for-patients/about-porphyria
2. Mokhatlo oa American Porphyria [Internet]. Houston: Motheo oa American Porphyria; c2010–2017. Porphyrins le Tlhatlhobo ea Porphyria; [e qotsitsoeng ka la 9 Tšitoe 26]; [li-skrini tse ka bang 6]. E fumaneha ho tsoa ho: https://www.porphyriafoundation.org/for-patients/about-porphyria/testing-for-porphyria/diagnosis
3. Mokhatlo oa American Porphyria [Internet]. Houston: Motheo oa American Porphyria; c2010–2017. Liteko tsa Mohala oa Pele; [e qotsitsoeng ka la 9 Tšitoe 26]; [hoo e ka bang li-skrini tse 4]. E fumaneha ho tsoa ho: https://www.porphyriafoundation.org/for-patients/about-porphyria/testing-for-porphyria/first-line-tests
4. Motheo oa Hepatitis B [Inthanete]. Doylestown (PA): Hepb.org; c2017. Lefu la Metabolic Mafu; [e qotsitsoeng ka la 2017 Tlhakubele 20]; [likhalase tse ka bang 11]. E fumaneha ho tsoa ho: http://www.hepb.org/research-and-programs/liver/risk-factors-for-liver-cancer/inherited-metabolic-diseases
5. Hinkle J, Cheever K. Brunner & Suddarth's Handbook ea Liteko tsa Laboraro le Tlhatlhobo. 2nd Ed, mosa. Philadelphia: Wolters Kluwer Bophelo, Lippincott Williams & Wilkins; c2014. Li-Porphyrin tse arohaneng tse arohaneng tsa Erythrocyte (FEP); leq. EA-308-TL.
6. Liteko tsa Lab Marang-rang [Inthaneteng]. Mokhatlo oa Amerika oa Clinical Chemistry; c2001–2017. Tlhaloso: Sampole ea Urine e sa Lebelloang; [e qotsitsoeng ka la 2017 Tlhakubele 20]; [li-skrini tse ka bang 3].E fumaneha ho tsoa ho: https://labtestsonline.org/glossary#r
7. Liteko tsa Lab Marang-rang [Inthaneteng]. Mokhatlo oa Amerika oa Clinical Chemistry; c2001–2017. Liteko tsa Porphyrin; [e ntlafalitsoeng 2017 Dec 20; e qotsitsoeng ka 2017 Phato 20]; [li-skrini tse ka bang 3]. E fumaneha ho tsoa ho: https://labtestsonline.org/tests/porphyrin-tests
8. Mayo Clinic [Inthaneteng]. Motheo oa Mayo oa Thuto ea Bongaka le Patlisiso; c1998–2017. Porphyria: Matšoao le Lisosa; 2017 Nov 18 [e qotsitsoeng ka 2017 Phato 20]; [li-skrini tse ka bang 3]. E fumaneha ho tsoa ho: https://www.mayoclinic.org/diseases-conditions/porphyria/symptoms-causes/syc-20356066
9. Mayo Clinic: Mayo Medical Laboratories [Inthaneteng]. Motheo oa Mayo oa Thuto ea Bongaka le Patlisiso; c1995–2017. ID ea Teko: FQPPS: Porphyrins, Mantle: Kakaretso; [e qotsitsoeng ka la 2017 Tlhakubele 20]; [li-skrini tse ka bang 2]. E fumaneha ho tsoa ho: https://www.mayomedicallaboratories.com/test-catalog/Overview/81652
10. Mayo Clinic: Mayo Medical Laboratories [Inthaneteng]. Motheo oa Mayo oa Thuto ea Bongaka le Patlisiso; c1995–2017. ID ea Teko: FQPPS: Porphyrins, Mantle: Mefuta; [e qotsitsoeng ka la 2017 Tlhakubele 20]; [li-skrini tse ka bang 3]. E fumaneha ho tsoa ho: https://www.mayomedicallaboratories.com/test-catalog/Specimen/81652
11. Phetolelo ea Merck Manual Consumer [Inthanete]. Kenilworth (NJ): Merck & Co Inc .; c2017. Porphyria e matla ea nakoana; [e qotsitsoeng ka la 2017 Tlhakubele 20]; [li-skrini tse ka bang 3]. E fumaneha ho tsoa ho: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorders/porphyrias/acute-intermittent-porphyria
12. Phetolelo ea Merck Manual Consumer [Inthanete]. Kenilworth (NJ): Merck & Co Inc .; c2017. Kakaretso ea Porphyria; [e qotsitsoeng ka la 2017 Tlhakubele 20]; [li-skrini tse ka bang 2]. E fumaneha ho tsoa ho: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorders/porphyrias/overview-of-porphyria
13. Phetolelo ea Merck Manual Consumer [Inthanete]. Kenilworth (NJ): Merck & Co Inc .; c2017. Porphyria Cutanea Tarda; [e qotsitsoeng ka la 2017 Tlhakubele 20]; [li-skrini tse ka bang 3]. E fumaneha ho tsoa ho: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorders/porphyrias/porphyria-cutanea-tarda
14. National Heart, Lung, le Setsi sa Mali [Internet]. Bethesda (MD): Lefapha la Bophelo le Litšebeletso tsa Botho la U.S. Liteko tsa Mali; [e qotsitsoeng ka la 2017 Tlhakubele 20]; [li-skrini tse ka bang 3]. E fumaneha ho tsoa ho: https://www.nhlbi.nih.gov/health-topics/blood-tests
15. Setsi sa Naha sa Lefu la Ts'oaetso le Mafu a Ts'oaetso le Liphio [Inthanete]. Bethesda (MD): Lefapha la Bophelo le Litšebeletso tsa Botho la U.S. Porphyria; 2014 Feb [e qotsitsoeng ka 2017 Phato 20]; [hoo e ka bang li-skrini tse 4]. E fumaneha ho tsoa ho: https://www.niddk.nih.gov/health-information/liver-disease/porphyria
16. Setsi sa Bongaka sa Rochester [Internet]. Rochester (NY): Setsi sa Bongaka sa Univesithi ea Rochester; c2017. Health Encyclopedia: Porphyrins (Moroto); [e qotsitsoeng ka la 2017 Tlhakubele 20]; [li-skrini tse ka bang 2]. E fumaneha ho tsoa ho: https://www.urmc.rochester.edu/encyclopedia/content.aspx?contenttypeid=167&contentid;=porphyrins_urine

Tlhahisoleseling e fumanehang sebakeng sena sa marang-rang ha ea lokela ho sebelisoa ho nka sebaka sa tlhokomelo ea bongaka le likeletso. Ikopanye le mofani oa tlhokomelo ea bophelo haeba u na le lipotso ka bophelo ba hau.