Sengoli: Morris Wright
Letsatsi La Creation: 24 April 2021
Ntlafatsa Letsatsi: 17 April 2025
Anonim
Ke eng le mokhoa oa ho phekola Becker muscular dystrophy - Bophelo
Ke eng le mokhoa oa ho phekola Becker muscular dystrophy - Bophelo

Litaba

Becker muscular dystrophy ke lefu la lefutso le bakang tšenyo ea butle-butle ea mesifa e mengata ea boithaopo, ke hore, mesifa eo re khonang ho e laola, joalo ka ea letheka, mahetla, maoto kapa matsoho, mohlala.

Hangata e atile haholo ho banna mme matšoao a pele a hlaha bongoaneng kapa nakong ea bocha, ho qala ka ho felloa ke matla hanyane ka hanyane hanyane hanyane hoo e batlang e le mesifa eohle ea 'mele, empa haholo mahetleng le lethekeng.

Le ha lefu lena le sena pheko, ho a khonahala ho ba le kalafo ea ho folisa matšoao le ho ba le bophelo bo botle le tebello ea bophelo ea lilemo tse ka bang 50.

Kalafo e etsoa joang

Kalafo ea Becker muscular dystrophy e etsoa ho fokotsa matšoao a motho e mong le e mong, ka hona, e ka fapana maemong ohle. Leha ho le joalo, mefuta e tloaelehileng ea kalafo e kenyelletsa:


  • Litlhare tsa Corticosteroid, joalo ka Betamethasone kapa Prednisone: thusa ho fokotsa ho ruruha ha mesifa ha o ntse o sireletsa likhoele tsa mesifa le bophahamo ba tsona. Ka tsela ena ho khonahala ho boloka ts'ebetso ea mesifa nako e telele;
  • Physiotherapy: e thusa ho boloka motsamao oa mesifa, ho e otlolla le ho e thibela hore e tiee haholo. Kahoo, ho ka khonahala ho fokotsa palo ea likotsi mesifa le manonyello a mesifa;
  • Phekolo ea mosebetsing: ke mananeo a rutang ho phela le meeli e mecha e bakoang ke lefu lena, ho koetlisa mekhoa e mecha ea ho etsa mesebetsi ea mantlha ea letsatsi le letsatsi e kang ho ja, ho tsamaea kapa ho ngola, mohlala.

Ntle le moo, ho ntse ho ka hlokahala hore u etse opereishene, haholo haeba mesifa e le khuts'oane kapa e le thata haholo, ho e lokolla le ho lokisa ho khutsufatsa. Ha likonteraka li hlaha ka har'a mesifa ea mahetla kapa morao, li ka baka ho holofala mokokotlong ho hlokang ho lokisoa ka ts'ebetso ea ts'ebetso.


Boemong bo matla ka ho fetisisa ba lefu lena, ho tloaelehile hore mathata a tebileng a hlahe, joalo ka mathata a pelo le ho hema ka thata, ka lebaka la ho senyeha ha mesifa ea pelo le mesifa ea ho hema. Maemong a joalo, ho ka khethoa ngaka ea pelo le pulmonologist ho thusa ho fetola kalafo.

Matšoao a mantlha

Matšoao a pele a Becker muscular dystrophy hangata a hlaha lipakeng tsa lilemo tse 5 ho isa ho tse 15, mme a ka kenyelletsa matšoao a kang:

  • Butle-butle bothata ba ho tsamaea le ho hloa litepisi;
  • Ho oela khafetsa ntle le lebaka;
  • Ho lahleheloa ke mesifa;
  • Ho fokola ha mesifa ea molala le matsoho;
  • Mokhathala o feteletseng;
  • Ho lahleheloa ke botsitso le khokahano;

Maemong a mangata ngoana a ka emisa ho tsamaea ho fihlela a le lilemo li 16, ha lefu lena le ntse le tsoela pele ka potlako maotong a ka tlase. Leha ho le joalo, ha matšoao a hlaha kamora nako e tloaelehileng, bokhoni ba ho tsamaea bo ka bolokoa le pakeng tsa lilemo tse 20 le 40.


Mokhoa oa ho hlahloba o etsoa joang

Maemong a mangata, ngaka ea bana e ka belaella mofuta ona oa ho senyeha habonolo feela ka ho hlahloba matšoao le ho shebella tahlehelo ea lisele tsa mesifa, mohlala. Leha ho le joalo, liteko tse ling tsa tlhatlhobo tse kang biopsy ea mesifa, liteko tsa pelo le X-ray li ka thusa ho netefatsa boteng ba Becker Muscular Dystrophy.

Ke eng e ka bakang lefu la ho fokola ha mmele

Becker's Muscular Dystrophy e hlaha ka lebaka la phetoho ea liphatsa tsa lefutso e thibelang tlhahiso ea protheine ea dystrophin, ntho ea bohlokoa haholo ho boloka lisele tsa mesifa li tsitsitse. Kahoo, ha protheine ena e le tlase 'meleng, mesifa ha e khone ho sebetsa hantle, e qala ho hlaha liso tse senyang likhoele tsa mesifa.

Joaloka lefu la lefutso, mofuta ona oa ho senyeha o ka fetisoa ho tloha ho batsoali ho ea ho bana kapa oa hlaha ka lebaka la phetoho nakong ea bokhachane.

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