Mokhoa oa ho phekola phenylketonuria le ho qoba mathata

Litaba

• 1. Kalafo ea phepo e nepahetseng
• Mokhoa oa ho fana ka lebese la matsoele ka polokeho
• 2. Ts'ebeliso ea litlatsetso tsa phepo
• Mathata a ka bang teng ha phenylketonuria
• Mokhoa oa ho qoba

Tlhokomelo le kalafo ea phenylketonuria ho lesea e lokela ho tataisoa ke ngaka ea bana, empa tlhokomelo ea mantlha ke ho qoba lijo tse nang le phenylalanine, tseo e leng lijo tse nang le liprotheine tse ngata joalo ka nama, tlhapi, lebese, chisi le mahe. Kahoo, batsoali ba masea a nang le phenylketonuria ba lokela ho ela hloko lijo tsa ngoana oa bona, lapeng le sekolong.

Ntle le moo, ho anyesa ka ho khetheha le hona ho lokela ho tataisoa ke ngaka ea bana, hobane lebese la matsoele le na le phenylalanine, leha e le tlase haholo ho feta e fumanoang mekhoeng e mengata ea litlama. Haele hantle, palo ea phenylalanine bakeng sa lesea ho fihlela likhoeli tse 6 e lokela ho bolokoa lipakeng tsa 20 ho isa ho 70 mg ea phenylalanine ka kg ea boima ba 'mele.

Ho bohlokoa hore kalafo ea phenylketonuria e lateloe ho latela tataiso ea ngaka ea bana le setsebi sa phepo e nepahetseng ho thibela mathata a hlahang, a amanang haholo le nts'etsopele ea sistimi ea methapo.

1. Kalafo ea phepo e nepahetseng

Kalafo ea phepo e nepahetseng ke tsela e ka sehloohong ea ho qoba mathata a lefu lena, hobane ke ka lijo ho ka khonehang ho laola maemo a phenylalanine maling, ka hona ho qoba mathata a lefu lena. Ho bohlokoa hore lijo li tataisoe ke setsebi sa phepo e nepahetseng ho latela liphetho tsa liteko tsa ngoana tse lokelang ho etsoa khafetsa ho lekola maemo a phenylalanine maling.

Phenylalanine e ka fumanoa lijong tse 'maloa, tsa liphoofolo le tsa meroho. Kahoo, ho laola lefu lena le ho qoba mathata ho bohlokoa ho qoba lijo tse ling, joalo ka:

• Lijo tsa liphoofolo: nama, lebese le lihlahisoa tsa nama, mahe, tlhapi, lijo tsa leoatleng, le lihlahisoa tsa nama tse kang boroso, boroso, bacon, ham.
• Lijo tsa semela: koro, soya le lihlahisoa, lierekisi, linaoa, lierekisi, lensisi, linate, matokomane, walnuts, lialmonde, makotomane, pistachios, linate tsa phaene;
• Li-sweeteners tse nang le aspartame;
• Lihlahisoa tse nang le lijo tse thibetsoeng e le motsoakojoalo ka likuku, cookies, ice cream le bohobe.

Litholoana le meroho li ka jeoa ke phenylketonurics, hammoho le tsoekere le mafura. Hape hoa khoneha ho fumana 'marakeng lihlahisoa tse ikhethileng tse' maloa tse etselitsoeng bamameli bana, joalo ka raese, pasta le li-crackers, 'me ho na le lipepe tse' maloa tse ka sebelisoang ho hlahisa lijo tse tlase ho phenylalanine.

Sheba lenane la lijo tse nang le phenylalanine.

Mokhoa oa ho fana ka lebese la matsoele ka polokeho

Le ha khothaletso e le ho kenyelletsa lebese la matsoele lijong tsa lesea, ho sebelisoa lebese la k'hemistri feela ntle le phenylalanine, ho ntse ho ka khoneha ho anyesa lesea phenylketonuric, leha ho le joalo ho hlokahala:

• Etsa tlhahlobo ea mali lesea beke e 'ngoe le e' ngoe ho lekola maemo a phenylalanine maling;
• Bala palo ea lebese leo u tla le fa lesea, ho latela boleng ba phenylalanine maling a ngoana le ho latela tataiso ea ngaka ea bana;
• Bala palo ea lebese la k'hemistri ntle le phenylalanine, ho phethela phepo ea lesea;
• Ka pompo, tlosa palo e nepahetseng ea lebese la 'm'a leo' m'a a ka le fang lesea;
• Sebelisa botlolo kapa mokhoa oa likamano ho fepa ngoana.

Ho bohlokoa ho khetholla amino acid phenylalanine lijong, e le hore lesea le se ke la ba le mathata kholong ea 'mele le kelellong, joalo ka ho holofala kelellong. Bona hore na lijo li lokela ho ba joang ho phenylketonuria.

2. Ts'ebeliso ea litlatsetso tsa phepo

Kaha lijo tsa motho ea nang le phenylketonuria li thibetsoe haholo, ho ka etsahala hore ha a na li-vithamine le liminerale tse ngata bakeng sa ts'ebetso e nepahetseng ea 'mele le kholo e nepahetseng ea ngoana. Kahoo, setsebi sa phepo e nepahetseng se ka khothaletsa ts'ebeliso ea litlatsetso le mekhoa ea phepo e nepahetseng ho netefatsa kholo e nepahetseng ea lesea le ho holisa bophelo ba lona.

Tlatsetso e lokelang ho sebelisoa e bonts'oa ke setsebi sa phepo ho latela lilemo, boima ba motho le matla a ts'ilo ea lesea, mme e tlameha ho bolokoa bophelo bohle.

Mathata a ka bang teng ha phenylketonuria

Mathata a phenylketonuria a hlaha ha tlhahlobo e sa etsoe kapele kapa ha kalafo e sa lateloe ho latela tataiso ea ngaka ea bana, ka ho bokella phenylalanine maling, e ka fihlelang libakeng tse ikhethileng tsa boko mme ea lebisa ntlafatsong ea liphetoho tse sa feleng, joalo ka joalo ka:

• Ho lieha nts'etsopele ea psychomotor;
• Khōlo e nyane ea boko;
• Microcephaly;
• Ho hloka botsitso;
• Mathata a boitšoaro;
• Fokotseha IQ;
• Khaello e tebileng ea kelello;
• Ho tsitsipana;
• Litšisinyeho.

Ha nako e ntse e tsamaea, haeba ngoana a sa alafshoe hantle, ho ka ba le bothata ba ho lula le ho tsamaea, mathata a boits'oaro le puo e liehang le kholo ea kelello, ntle le khatello ea maikutlo, lefu la sethoathoa le ataxia, e leng tahlehelo ea taolo ea metsamao ea boithatelo.

Mokhoa oa ho qoba

Ho qoba mathata, ho bohlokoa hore tlhahlobo ea lefu lena e etsoe matsatsing a pele kamora ho hlaha ha ngoana ka tlhahlobo ea serethe. Haeba sephetho se le hantle, ho bohlokoa hore kalafo e etsoe ho latela tataiso ea ngaka ea bana.

Ntle le moo, maemong ana ho bohlokoa hore litlhahlobo tse etsoang khafetsa li hlahlojoe bophelo bo botle ba ngoana, ka hona, ho bonts'a liphetoho lijong le lijong tse tlatselletsang.

Litlhahlobo tse latelang li etsoa beke le beke ho fihlela ngoana a le lilemo li 1. Bana ba pakeng tsa lilemo tse 2 ho isa ho tse 6 ba pheta tlhatlhobo matsatsing a mang le a mang a 15 mme ho tloha lilemong tse 7 tlhatlhobo e etsoa hang ka khoeli.