Acid mucopolysaccharides

Acid mucopolysaccharides ke teko e lekanyang palo ea mucopolysaccharides e ntšitsoeng ka morong ka nako ea ketsahalo e le 'ngoe kapa ka nako ea lihora tse 24.

Mucopolysaccharides ke liketane tse telele tsa limolek'hule tsa tsoekere 'meleng. Hangata li fumanoa ka har'a mameno le mokelikeli o potileng manonyeletso.

Bakeng sa teko ea lihora tse 24, o tlameha ho ntša metsi ka mokotleng kapa setsing se khethehileng nako le nako ha o sebelisa ntloana. Hangata, o tla fuoa lijana tse peli. U tla ntša metsi ka kotloloho ka har'a setshelo se ikhethang ebe u fetisetsa moroto oo ka setshelong se seng se seholoanyane.

• Ka letsatsi la 1, ntša metsi ka ntloaneng ha u tsoha hoseng.
• Kamor'a ho ntša metsi pele, ntša metsi ka har'a setshelo se khethehileng nako le nako ha u sebelisa ntloana bakeng sa lihora tse 24 tse latelang. Fetisetsa moroto ka har'a setshelo se seholo ebe u boloka setshelo se seholoanyane sebakeng se phodileng kapa ka sehatsetsing. Boloka setshelo sena se koetsoe ka thata.
• Ka letsatsi la bobeli, ntša metsi ka setshelong hoseng hape ha u tsoha ebe u fetisetsa moroto ona ka setshelong se seholoanyane.
• Tšoaea setshelo se seholoanyane ka lebitso la hau, letsatsi, nako ea ho phethela, 'me u se khutlise kamoo u laetsoeng kateng.

Bakeng sa lesea:

Hlatsoa ka botlalo sebaka se potileng urethra (lesoba leo moroto o phallelang ho lona). Bula mokotla oa pokello ea moroto (mokotla oa polasetiki o nang le pampiri e khomarelang ka lehlakoreng le leng).

• Bakeng sa banna, kenya botona kaofela ka mokotleng ebe u hokela pampiri e khomarelang letlalong.
• Bakeng sa basali, beha mokotla holim 'a mapheo a mabeli a letlalo ka lehlakoreng le leng la botshehadi (labia). Beha leleiri holim'a lesea (ka holim'a mokotla).

Lekola lesea khafetsa, 'me u chenche mokotla ha lesea le qeta ho ntša metsi. Tlosa moroto ka mokotleng ebe o o kenya ka setshelong se fanoeng ke mofani oa tlhokomelo ea bophelo.

Masea a mahlahahlaha a ka tsamaisa mokotla, a etsa hore moroto o kene leletseng. U kanna ua hloka mekotla e mengata ea pokello.

Ha u qetile, tšoaea setshelo ebe u se khutlisa kamoo u laetsoeng kateng.

Ha ho na litokisetso tse khethehileng tse hlokahalang.

Teko e kenyelletsa feela ho rota ho tloaelehileng, 'me ha ho na bothata.

Teko ena e etsoa ho fumana sehlopha se sa tloaelehang sa maloetse se bitsoang mucopolysaccharidoses (MPS). Tsena li kenyelletsa, Hurler, Scheie, le Hurler / Scheie syndromes (MPS I), Hunter syndrome (MPS II), Sanfilippo syndrome (MPS III), Morquio syndrome (MPS IV), Maroteaux-Lamy syndrome (MPS VI), le Sly syndrome (MPS VII).

Boholo ba nako, tlhahlobo ena e etsoa ho masea a ka bang le letšoao kapa nalane ea lelapa la a mang a mathata ana.

Maemo a tloaelehileng a fapana ho ea ka lilemo le ho tloha lab ho ea lab. Bua le mofani oa hau ka moelelo oa sephetho sa hau sa liteko.

Maemo a phahameng ka mokhoa o sa tloaelehang a ka tsamaellana le mofuta oa mucopolysaccharidosis. Ho hlokahala liteko tse ling ho fumana mofuta o khethehileng oa mucopolysaccharidosis.

AMP; Dermatan sulfate - moroto; Moroto heparan sulfate; Moroto dermatan sulfate; Heparan sulfate - moroto

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