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Letsatsi La Creation: 8 Phato 2021
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Ho hloka mamello ea lefa la fructose - Moriana
Ho hloka mamello ea lefa la fructose - Moriana

Ho se mamellane ha lefa la fructose ke lefu leo ​​ho lona motho a haelloang ke protheine e hlokahalang ho senya fructose. Fructose ke tsoekere ea litholoana eo ka tlhaho e hlahang 'meleng. Fructose e entsoeng ke motho e sebelisoa e le sejo se monate lijong tse ngata, ho kenyeletsoa lijo tsa bana le lino.

Boemo bona bo etsahala ha 'mele o haelloa ke enzyme e bitsoang aldolase B. Ntho ena ea hlokahala ho senya fructose.

Haeba motho ea se nang ntho ena a ja fructose kapa sucrose ('moba kapa beet tsoekere, tsoekere ea tafoleng), liphetoho tse rarahaneng tsa lik'hemik'hale li etsahala' meleng. 'Mele o ke ke oa fetola mofuta oa tsoekere o bolokiloeng (glycogen) hore e be tsoekere. Ka lebaka leo, tsoekere maling e oa le lintho tse kotsi sebeteng.

Ho se mamellane ha lefa la fructose ho futsitsoe, ho bolelang hore e ka fetisoa ka malapa. Haeba batsoali ka bobeli ba na le kopi e sa sebetseng ea lefutso la aldolase B, ngoana e mong le e mong oa bona o na le monyetla oa ho ameha ka 25% (1 ho 4).

Matšoao a ka bonoa kamora hore ngoana a qale ho ja lijo kapa lebese le phofo.


Matšoao a pele a ho hloka mamello ha fructose a tšoana le a galactosemia (ho se khone ho sebelisa tsoekere galactose). Matšoao a morao a amana haholo le lefu la sebete.

Matšoao a ka kenyelletsa:

  • Ho tsitsinyeha
  • Ho robala haholo
  • Ho teneha
  • Letlalo le mosehla kapa makhooa a mahlo (jaundice)
  • Ho fepa le ho hola hampe joaloka lesea, ho hloleha ho phela hantle
  • Mathata kamora ho ja litholoana le lijo tse ling tse nang le fructose kapa sucrose
  • Ho hlatsa

Tlhahlobo ea 'mele e ka bontša:

  • Ho eketsa sebete le spleen
  • Jaundice

Liteko tse netefatsang lefu lena li kenyelletsa:

  • Liteko tsa ho koala mali
  • Teko ea tsoekere ea mali
  • Lithuto tsa enzyme
  • Ho etsa liteko tsa lefutso
  • Liteko tsa ts'ebetso ea liphio
  • Liteko tsa ts'ebetso ea sebete
  • Biopsy ea sebete
  • Teko ea mali ea Uric acid
  • Ho hlahloba urinal

Tsoekere ea mali e tla ba tlase, haholo kamora ho amohela fructose kapa sucrose. Maemo a acid ea Uric a tla ba holimo.

Ho tlosa fructose le sucrose lijong ke kalafo e sebetsang ho batho ba bangata. Mathata a ka phekoloa. Mohlala, batho ba bang ba ka noa moriana ho theola boemo ba asiti ea uric maling a bona le ho fokotsa menyetla ea ho tšoaroa ke gout.


Ho hloka mamello ea fructose e ka ba bonolo kapa e matla.

Ho qoba fructose le sucrose ho thusa bana ba bangata ba nang le boemo bona. Phatlalatso e ntle maemong a mangata.

Bana ba 'maloa ba nang le mofuta o matla oa lefu lena ba tla ba le lefu le matla la sebete. Esita le ho tlosa fructose le sucrose lijong ho ka 'na ha se ke ha thibela lefu le matla la sebete ho bana bana.

Hore na motho o sebetsa hantle hakae ho latela:

  • Ho fumanoa kapele hakae
  • Haufinyane fructose le sucrose li ka tlosoa lijong joang
  • Enzyme e sebetsa hantle hakae 'meleng

Mathata ana a ka hlaha:

  • Ho qoba lijo tse nang le fructose ka lebaka la litlamorao
  • Ho tsoa mali
  • Gout
  • Ho kula ka ho ja lijo tse nang le fructose kapa sucrose
  • Ho hloleha ha sebete
  • Tsoekere e tlase ea mali (hypoglycemia)
  • Ho oa
  • Lefu

Bitsa mofani oa tlhokomelo ea bophelo haeba ngoana oa hau a ba le matšoao a boemo bona kamora ho fepa ho qala. Haeba ngoana oa hau a na le boemo bona, litsebi li khothaletsa ho bona ngaka e sebetsanang le liphatsa tsa lefutso tsa liphatsa tsa lefutso kapa metabolism.


Banyalani ba nang le nalane ea lelapa ea ho hloka mamello ha fructose ba lakatsang ho ba le ngoana ba ka nahana ka tlhabollo ea lefutso.

Boholo ba litlamorao tse mpe tsa lefu lena li ka thibeloa ka ho fokotsa ho ja ha fructose le sucrose.

Fructosemia; Ho hloka mamello ha Fructose; Fructose aldolase B-khaello; Ho haella ha Fructose-1, 6-bisphosphate aldolase

Bonnardeaux A, Bichet DG. Mathata a futsitsoeng a renal tubule. Ka: Skorecki K, Chertow GM, Marsden PA, Taal MW, Yu ASL, li-eds. Brenner le Rector ea Liphio. 10th ed. Philadelphia, PA: Elsevier; 2016: khaolo ea 45.

Kishnani PS, Chen YT. Liphoso tsa metabolism ea lik'habohaedreite. Ka: Kliegman RM, St. Geme JW, Schor NF, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Buka ea Nelson ea Pediatrics. La 21 Ed. Philadelphia, PA: Elsevier; 2020: khaolo ea 105.

Nadkarni P, Weinstock RS. Likhabohaedreite. Ka: McPherson RA, Pincus MR, bahlophisi. Henry's Clinical Diagnosis le Tsamaiso ka Mekhoa ea Laboraro. La bo23 la ed. St Louis, MO: Elsevier; 2017: khaolo ea 16.

Scheinman SJ. Mathata a ho tsamaisa liphio ka liphatsa tsa lefutso. Ka: Gilbert SJ, Weiner DE, bahlophisi. Mokhatlo oa National Kidney Foundation oa Mafu a Liphio. La 7th. Philadelphia, PA: Elsevier; 2018: khaolo ea 38.

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