Birt-Hogg-Dubé lefu

Litaba

• Litšoantšo tsa Birt-Hogg-Dubé Syndrome
• Matšoao a Birt-Hogg-Dubé Syndrome
• Kalafo ea Birt-Hogg-Dubé Syndrome
• Lihokelo tse sebetsang:

Birt-Hogg-Dubé Syndrome ke lefu le sa tloaelehang la liphatsa tsa lefutso le bakang liso tsa letlalo, lihlahala tsa liphio le li-cyst matšoafong.

Ka lisosa tsa Birt-Hogg-Dubé Syndrome ke liphetoho liphatseng tsa lefutso tsa chromosome 17, e bitsoang FLCN, e lahleheloang ke ts'ebetso ea eona e le khatello ea hlahala mme e lebisa ho hlaheng ha lihlahala ho batho ka bomong.

THE Birt-Hogg-Dubé lefu ha le na pheko mme kalafo ea eona e na le ho tlosa lihlahala le ho thibela ponahalo ea tsona.

Litšoantšo tsa Birt-Hogg-Dubé Syndrome

Lifotong u ka tseba liso tsa letlalo tse hlahang ho Birt-Hogg-Dubé Syndrome, e hlahisang lihlahala tse nyane tse bohloko tse bopehang haufi le moriri.

Matšoao a Birt-Hogg-Dubé Syndrome

Matšoao a Birt-Hogg-Dubé Syndrome e ka ba:

• Lihlahala tsa Benign letlalong, haholo sefahleho, molala le sefuba;
• Li-cysts tsa renal;
• Lihlahala tsa liphio tsa Benign kapa mofetše oa liphio;
• Li-cysts tsa pulmonary;
• Ho bokellana ha moea lipakeng tsa matšoafo le mokokotlo, ho lebisang ponahalong ea pneumothorax;
• Maqhutsu a qoqotho.

Batho ba nang le Birt-Hogg-Dubé Syndrome ba na le monyetla oa ho tšoaroa ke mofetše likarolong tse ling tsa 'mele joalo ka letsoele, amygdala, matšoafo kapa mala.

Liso tse hlahang letlalong li bitsoa fibrofolliculomas 'me li na le lihloba tse nyane tse bakoang ke ho bokellana ha collagen le likhoele tse potileng moriri. Ka kakaretso, letšoao lena letlalong la Birt-Hogg-Dubé Syndrome le hlaha lipakeng tsa lilemo tse 30 le 40.

O Ho fumanoa ha Birt-Hogg-Dubé Syndrome e fihlelleha ka ho supa matšoao a lefu lena le liteko tsa lefutso ho supa phetoho liphatseng tsa lefutso tsa FLNC.

Kalafo ea Birt-Hogg-Dubé Syndrome

Kalafo ea Birt-Hogg-Dubé Syndrome ha e phekole lefu lena, empa e thusa ho fokotsa matšoao le litlamorao tsa lona maphelong a batho ka bomong.

Lihlahala tsa Benign tse hlahang letlalong li ka tlosoa ka bongaka, dermo-abrasion, laser kapa letlalo.

Li-cysts tsa pulmonary kapa lihlahala tsa liphio li tlameha ho thibeloa ka tlhahlobo ea k'homphieutha, matla a khoheli kapa liteko tsa ultrasound. Haeba boteng ba li-cysts kapa lihlahala li fumanoa litekong, li tlameha ho tlosoa.

Maemong ao mofets'e oa liphio o hlahang, kalafo e lokela ho ba le ts'ebetso ea ho buuoa, chemotherapy kapa kalafo ea radiation.

Lihokelo tse sebetsang:

• Cyst ea liphio
• Pneumothorax