Lefa spherocytosis: lisosa, matšoao le kalafo

Litaba

• Spherocytosis e bakoa ke eng
• Matšoao a mantlha
• Kalafo e etsoa joang

Hereditary spherocytosis ke lefu la lefutso le khetholloang ke liphetoho liseleng tse khubelu tsa lisele tsa mali, tse lumellang tšenyo ea lona, ​​ka hona le nkuoa e le phokolo ea mali ea hemolytic. Liphetoho lera la lisele tse khubelu tsa mali li li etsa tse nyane le tse hanyetsanang ho feta tloaelo, li senyeha habonolo ke spleen.

Spherocytosis ke lefu le futsitsoeng, le tsamaeang le motho ho tloha tsoalong, empa le ka tsoela pele ka phokolo ea mali e fapaneng haholo. Kahoo, maemong a mang ho kanna ha se be le matšoao mme ho a mang, pallor, mokhathala, jaundice, spleen e atolositsoeng le liphetoho tsa kholo, mohlala, li ka bonahala.

Le ha ho se na pheko, spherocytosis e na le kalafo, e lokelang ho tataisoa ke setsebi sa methapo ea mali, 'me phetisetso ea folic acid e ka bonts'oa,' me maemong a thata ka ho fetisisa, ho tlosoa spleen, e bitsoang splenectomy, molemong oa ho laola lefu lena .

Spherocytosis e bakoa ke eng

Lefutso spherocytosis le bakoa ke phetoho ea liphatsa tsa lefutso e hlahisang phetoho ea bongata kapa boleng ba liprotheine tse etsang lisele tsa lisele tse khubelu tsa mali, tse tsejoang ka hore ke lisele tse khubelu tsa mali. Liphetoho liprotheine tsena li baka tahlehelo ea ho tenyetseha le ts'ireletso ea lisele tse khubelu tsa lisele tsa mali, tse li etsang hore li senyehe habonolo le ho ba tse nyane, leha litaba li le joalo, li etsa lisele tse khubelu tse nyane, tse nang le sebopeho se chitja le tse nang le 'mala o mongata.

Phokolo ea mali e hlaha hobane li-spherocyte, joalo ka ha lisele tse khubelu tse holofetseng li bitsoa spherocytosis, hangata li senngoa ke spleen, haholo-holo ha liphetoho li le bohlokoa mme ho na le tahlehelo ea maemo le ho hana ho feta ka microcirculation ea mali ho tsoa setho sena.

Matšoao a mantlha

Spherocytosis e ka hlalosoa e le bonolo, e itekanetseng kapa e matla. Kahoo, batho ba nang le spherocytosis e bonolo ba kanna ba se be le matšoao, athe ba nang le spherocytosis e itekanetseng ho isa ho e matla ba ka ba le matšoao le matšoao a fapaneng joalo ka:

• Pheello ea mali;
• Pallor;
• Ho khathala le ho se mamelle boikoetliso ba 'mele;
• Ho eketsa bilirubin maling le jaundice, e leng 'mala o mosehla oa letlalo le lisele tsa mucous;
• Ho theha majoe a bilirubin ka har'a gallbladder;
• Boholo ba spleen.

Bakeng sa ho fumana lefutso la spherocytosis, ntle le tlhahlobo ea bongaka, ngaka ea mali e ka laela liteko tsa mali joalo ka palo ea mali, palo ea reticulocyte, tekanyo ea bilirubin le smear ea mali e bonts'ang liphetoho tse hlahisang mofuta ona oa phokolo ea mali.Ho boetse ho bontšoa tlhahlobo ea "osmotic fragility", e lekanyang khanyetso ea lera le khubelu la lisele tsa mali.

Kalafo e etsoa joang

Hereditary spherocytosis ha e na pheko, leha ho le joalo, ngaka ea mali e ka khothaletsa kalafo e ka fokotsang ho mpefala ha lefu le matšoao, ho latela litlhoko tsa mokuli. Tabeng ea batho ba sa bontšeng matšoao a lefu lena, ha ho hlokahale kalafo e khethehileng.

Phetoho ea asiti ea folic e khothaletsoa hobane, ka lebaka la ho senyeha ho eketsehileng ha lisele tse khubelu tsa mali, ntho ena e hlokahala haholo bakeng sa ho theoa ha lisele tse ncha tsa moko.

Mofuta oa mantlha oa kalafo ke ho tlosa spleen ka ho buuoa, hangata ho bonts'ang ho bana ba ka holimo ho lilemo tse 5 kapa tse 6 ba nang le phokolo ea mali e matla joalo ka ba nang le hemoglobin e ka tlase ho 8 mg / dl palong ea mali, kapa ka tlase ho 10 mg / dl haeba ho na le matšoao a bohlokoa kapa mathata a kang a majoe a senya. Ho buuoa ho ka etsoa hape ho bana ba nang le tieho ea kholo ka lebaka la lefu lena.

Batho ba tlosoang ke spleen ba na le monyetla oa ho ba le ts'oaetso e itseng kapa li-thromboses, ka hona liente, joalo ka pneumococcal, lia hlokahala, ntle le ts'ebeliso ea ASA ho laola ho koala mali. Hlahloba hore na ho etsoa opereishene ea ho tlosa spleen le tlhokomelo e hlokahalang ho etsoa joang.