Sengoli: Clyde Lopez
Letsatsi La Creation: 17 Phupu 2021
Ntlafatsa Letsatsi: 5 Hlakubele 2025
Anonim
Teko ea mali ea Methylmalonic acid - Moriana
Teko ea mali ea Methylmalonic acid - Moriana

Teko ea mali ea methylmalonic acid e lekanya palo ea methylmalonic acid maling.

Ho hlokahala sampole ea mali.

Ha ho litokisetso tse khethehileng tse hlokahalang.

Ha nale e kentsoe ho hula mali, batho ba bang ba utloa bohloko bo itekanetseng. Ba bang ba ikutloa feela ho hlaba kapa ho hlaba. Kamora moo, ho kanna ha ba le ho longoa kapa ho longoa hanyenyane. Haufinyane sena sea fela.

Methylmalonic acid ke ntho e hlahisoang ha liprotheine, tse bitsoang liamino acid, 'meleng li senyeha.

Mofani oa tlhokomelo ea bophelo a ka laela tlhahlobo ena haeba ho na le matšoao a mafu a itseng a liphatsa tsa lefutso, joalo ka methylmalonic acidemia. Ho lekoa bakeng sa lefu lena hangata ho etsoa e le karolo ea tlhahlobo ea masea e sa tsoa tsoaloa.

Teko ena e kanna ea etsoa ka liteko tse ling ho lekola khaello ea vithamine B12.

Litekanyetso tse tloaelehileng ke li-micromoles tse 0,07 ho isa ho 0,27 ka litara.

Mekhahlelo e tloaelehileng ea boleng e ka fapana hanyane hara lilaboratori tse fapaneng. Li-lab tse ling li sebelisa litekanyo tse fapaneng kapa li leka liteko tse fapaneng. Bua le ngaka ea hau ka se boleloang ke sephetho sa hau sa liteko.


Boleng bo phahameng ho feta bo tloaelehileng e ka ba ka lebaka la khaello ea vithamine B12 kapa methylmalonic acidemia.

Ha ho na kotsi e kholo ea ho nkuoa mali a hau. Methapo le methapo li fapana ka boholo ho tloha ho motho e mong ho ea ho o mong le ho tloha lehlakoreng le leng la 'mele ho ea ho le leng. Ho nka mali ho batho ba bang ho ka ba thata ho feta ho ba bang.

Likotsi tse ling tse amanang le ho huloa mali li nyane, empa li ka kenyelletsa:

  • Ho akheha kapa ho ikutloa o le hlooho e boima
  • Li-punctures tse ngata ho fumana methapo
  • Hematoma (mali a hahiloeng ka tlas'a letlalo)
  • Ho tsoa mali a mangata
  • Tšoaetso (kotsi e nyane neng kapa neng ha letlalo le robehile)
  • Teko ea mali

Antony AC. Li-anemias tsa Megaloblastic. Ka: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Melao-motheo le Tloaelo ea Motheo. La 7th. Philadelphia, PA: Elsevier; 2018: khaolo ea 39.


Elghetany MT, Schexneider KI, mathata a Banki K. Erythrocytic. Ka: McPherson RA, Pincus MR, bahlophisi. Henry's Clinical Diagnosis le Tsamaiso ka Mekhoa ea Laboraro. La bo23 la ed. St Louis, MO: Elsevier; 2017: khaolo ea 32.

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