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Letsatsi La Creation: 20 September 2021
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An Overview of Hereditary Haemorrhagic Telangiectasia (HHT) by Prof Claire Shovlin
Video: An Overview of Hereditary Haemorrhagic Telangiectasia (HHT) by Prof Claire Shovlin

Telangiectasias ke methapo e menyenyane ea mali e atolositsoeng letlalong. Hangata ha li na kotsi, empa li ka amahanngoa le mafu a 'maloa.

Telangiectasias e ka hlaha kae kapa kae kahare ho mmele. Empa li bonoa habonolo letlalong, lera la 'mele le ho soeufala ha mahlo. Hangata, ha li bake matšoao. Tse ling tsa telangiectasias li tsoa mali mme li baka mathata a maholo. Telangiectasias le eona e ka hlaha bokong kapa mala mme ea baka mathata a maholo ho tsoa mali.

Lisosa li ka kenyelletsa:

  • Rosacea (bothata ba letlalo bo etsang hore sefahleho se khubelu)
  • Ho tsofala
  • Bothata ba liphatsa tsa lefutso
  • Boimana
  • Ho pepeseha ha letsatsi
  • Metsing ea varicose
  • Tšebeliso e feteletseng ea litlolo tsa steroid
  • Matšoenyeho sebakeng seo

Maloetse a amanang le boemo bona a kenyelletsa:

  • Ataxia-telangiectasia (lefu le amang letlalo, tekano le tšebelisano, le likarolo tse ling tsa 'mele)
  • Bloom syndrome (lefu le futsitsoeng le bakang sekhahla se khuts'oane, kutlo ea letlalo mahlaseling a letsatsi le bofubelu ba sefahleho)
  • Cutis marmorata telangiectatica congenita (lefu la letlalo le bakang likhahla tse khubelu)
  • Lefu la hemorrhagic telangiectasia (Osler-Weber-Rendu lefu)
  • Klippel-Trenaunay-Weber syndrome (lefu le bakang letheba la veine ea port, methapo ea varicose le mathata a lisele tse bonolo)
  • Nevus flammeus joalo ka letheba la veine ea port
  • Rosacea (boemo ba letlalo bo bakang bofubelu ba sefahleho)
  • Lefu la Sturge-Weber (lefu le amanang le letheba la veine ea port le mathata a sistimi ea methapo)
  • Xeroderma pigmentosa (lefu leo ​​letlalo le lisele tse koahelang leihlo li amehang haholo ka leseli la mahlaseli a kotsi)
  • Lupus (lefu la sesole sa 'mele)
  • CREST syndrome (mofuta oa scleroderma o kenyelletsang ho bokellana ha lisele tse kang lebali letlalong le kae kapa kae 'meleng le ho senya lisele tse moeling oa methapo e menyenyane)

Bitsa mofani oa hao oa tlhokomelo ea bophelo haeba u bona lijana tse atolositsoeng letlalong, manong a mahlo kapa mahlong.


Mofani oa hau o tla etsa tlhahlobo ea 'mele' me a botse ka matšoao a hau, ho kenyelletsa:

  • Methapo ea mali e fumaneha kae?
  • Na ba tsoa mali habonolo le ntle le lebaka?
  • Ke matšoao afe a mang a teng?

Liteko li kanna tsa hlokahala ho fumana kapa ho thibela boemo ba bongaka. Liteko li ka kenyelletsa:

  • Liteko tsa mali
  • Lisebelisoa tsa CT
  • Lithuto tsa ts'ebetso ea sebete
  • MRI e hlahloba
  • Li-X-ray

Sclerotherapy ke kalafo ea telangiectasias maotong. Ts'ebetsong ena, tharollo ea letsoai (letsoai) kapa lik'hemik'hale tse ling li kenoa ka kotloloho methapong ea sekho maotong. Kalafo ea laser e tloaetse ho sebelisoa ho phekola telangiectasias ea sefahleho.

Li-ectasias tsa mesifa; Sekho se angioma

  • Angioma serpiginosum
  • Telangiectasia - maoto
  • Telangiectasias - letsoho le kaholimo

Kelly R, Baker C. Mathata a mang a methapo. Ka: Bolognia JL, Schaffer JV, Cerroni L, bahlophisi. Dermatology. La 4 ed. Philadelphia, PA: Elsevier; 2018: khaolo ea 106.


Patterson JW. Lihlahala tsa vascular. Ka: Patterson JW, e hlophisitsoeng. Bolwetse ba Letlalo la Weedon. La 4 ed. Philadelphia, PA: Elsevier Churchill Livingstone; 2016: khaolo ea 38.

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