Biliary atresia

Biliary atresia ke thibelo ea li-tubes (ducts) tse tsamaisang mokelikeli o bitsoang bile ho tloha sebeteng ho ea ho gallbladder.

Biliary atresia e hlaha ha methapo ea bile kahare kapa kantle ho sebete e le moqotetsane ka mokhoa o sa tloaelehang, e koetsoe kapa e le sieo. Methapo ea bile e na le mokelikeli o silang lijo ho tloha sebeteng ho ea maleng a manyane ho senya mafura le ho sefa litšila 'meleng.

Lebaka la lefu lena ha le hlake hantle. E kanna ea ba ka lebaka la:

• Tšoaetso ea vaerase kamora 'tsoalo
• Ho pepesehela lintho tse chefo
• Lintho tse ngata tsa lefutso
• Kotsi ea Perinatal
• Meriana e meng e kang carbamazepine

Hangata e ama batho ba litloholo tsa Asia Bochabela le Afrika le Amerika.

Methapo ea bile e thusa ho tlosa litšila sebeteng le ho tsamaisa matsoai a thusang mala a manyane ho theola mafura.

Ho masea a nang le biliary atresia, noka e tsoang sebeteng ho ea ho gallbladder e koetsoe. Sena se ka baka tšenyo ea sebete le ho thatafala ha sebete, tse ka bang kotsi.

Matšoao hangata a qala ho hlaha lipakeng tsa libeke tse 2 ho isa ho tse 8. Jaundice ('mala o mosehla letlalong le lisele tsa mameno) e qala butle butle libeke tse 2 ho isa ho tse 3 kamora ho hlaha. Lesea le ka ba le boima bo tloaelehileng khoeling ea pele. Kamora moo, lesea le tla theola boima ba 'mele ebe lea teneha,' me le tla mpefala le jaundice.

Matšoao a mang a kenyeletsa:

• Moroto o lefifi
• Mpa e ruruhileng
• Litulo tse nkhang hampe le tse phaphametseng
• Litulo tse pente kapa tse 'mala oa letsopa
• Khōlo e liehang

Mofani oa hao oa tlhokomelo ea bophelo o tla nka nalane ea bongaka ea ngoana oa hau mme a etse tlhahlobo ea 'mele ho lekola sebete se atolositsoeng.

Liteko tsa ho fumana biliary atresia li kenyelletsa:

• X-ray ea mpeng ho hlahloba sebete le spleen e atolositsoeng
• Mpa ea mpa ea mpa ho hlahloba litho tsa ka hare
• Liteko tsa mali ho lekola litekanyetso tsa bilirubin ka botlalo le ka kotloloho
• Hepatobiliary scintigraphy kapa HIDA e hlahloba ho bona hore na methapo ea bile le gallbladder li sebetsa hantle
• Biopsy ea sebete ho lekola ho teba ha lefu la ho thatafala ha pelo kapa ho felisa lisosa tse ling tsa jaundice
• X-ray ea methapo ea bile (cholangiogram) ho netefatsa hore na methapo ea bile e butsoe kapa e koetsoe

Ts'ebetso e bitsoang ts'ebetso ea Kasai e etsoa ho hokahanya sebete le mala a manyane. Litsela tse sa tloaelehang li feta. Ho buuoa ho atleha haholo haeba ho etsoa pele lesea le e-na le libeke tse 8.

Ho kenyelletsa sebete ho ka 'na ha hlokahala pele ho lilemo tse 20 maemong a mangata.

Ho buuoa kapele ho tla ntlafatsa pholoho ea masea a fetang karolo ea boraro ea bana ba nang le boemo bona. Melemo ea nako e telele ea ho kenyelletsa sebete ha e so tsejoe, empa ho lebelletsoe hore e ntlafatse bophelo.

Mathata a ka kenyelletsa:

• Tšoaetso
• Cirrhosis e ke keng ea qojoa
• Ho hloleha ha sebete
• Mathata a ho buoa, ho kenyeletsoa ho hloleha hoa ts'ebetso ea Kasai

Bitsa mofani oa hau haeba ngoana oa hau a bonahala a le jaundiced, kapa haeba matšoao a mang a biliary atresia a hlaha.

Lesea le sa tsoa tsoaloa - biliary atresia; Lesea le sa tsoa tsoaloa - biliary atresia; Extrahepatic ductopenia; Ts'ebetso e tsoelang pele ea "cholangiopathy"

• Lefu la masea le sa tsoa tsoaloa - ho tsoa
• Lefu le sa tsoa tsoaloa - seo u lokelang ho se botsa ngaka ea hau

• Bile e hlahisoa sebeteng

Berlin SC. Papiso ea ho tseba ea bocha. Ka: Martin RJ, Fanaroff AA, Walsh MC, bangoli. Fanaroff le Phekolo ea Martin ea Neonatal-Perinatal. 11th ed. Philadelphia, PA: Elsevier; 2020: khaolo ea 38.

Cazares J, Ure B, Yamataka A. Biliary atresia. Ka: Holcomb GW, Murphy JP, Mohalaleli Peter SD, eds. Phekolo ea bana ea Holcomb le Ashcraft. La 7th. Philadelphia, PA: Elsevier; 2020: khaolo ea 43.

Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Mosebetsi RC. Cholestasis. Ka: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, bahlophisi. Buka ea Nelson ea Pediatrics. La 21 Ed. Philadelphia, PA: Elsevier; 2020: khaolo ea 383.

O'Hara SM. Sebete sa bana le spleen. Ka: Rumack CM, Levine D, eds. Tlhahlobo ea Ultrasound. La 5th. Philadelphia, PA: Elsevier; 2018: khaolo ea 51.