Lefu la Klippel-Trenaunay

Klippel-Trenaunay syndrome (KTS) ke boemo bo sa tloaelehang bo atisang ho ba teng ha motho a hlaha. Lefu lena hangata le kenyelletsa mabala a veine ea koung, kholo e feteletseng ea masapo le lisele tse bonolo, le methapo ea varicose.

Maemong a mangata a KTS a etsahala ntle le lebaka le hlakileng. Leha ho le joalo, linyeoe tse 'maloa li nahanoa hore li fetisoa ka malapa (a futsitsoeng).

Matšoao a KTS a kenyelletsa:

• Matheba a mangata a veine ea koung kapa mathata a mang a methapo ea mali, ho kenyeletsoa matheba a lefifi letlalong
• Metsing ea varicose (e ka bonoa ho tloha boseeng, empa e ka bonahala hamorao bongoaneng kapa bocheng)
• Tsela e sa tsitsang ka lebaka la phapang ea bolelele ba maoto le matsoho (karolo e amehang e telele)
• Bohloko ba masapo, methapo kapa methapo

Matšoao a mang a ka bang teng:

• Ho tsoa mali ho tsoa ho rectum
• Mali ka morong

Batho ba nang le boemo bona ba ka ba le kholo e feteletseng ea masapo le lisele tse bonolo. Sena se etsahala hangata maotong, empa se ka ama le matsoho, sefahleho, hlooho kapa litho tsa ka hare.

Mekhoa e fapaneng ea ho nka litšoantšo e ka sebelisoa ho fumana phetoho efe kapa efe mohahong oa 'mele ka lebaka la boemo bona. Tsena li thusa ho etsa qeto ea moralo oa kalafo. Tsena li ka kenyelletsa:

• MRA
• Phekolo ea Endoscopic Thermal Ablation Therapy
• Li-X-ray
• Lisebelisoa tsa CT kapa CT venography
• MRI
• Colour duplex ultrasonography

Ultrasound nakong ea bokhachane e ka thusa ho fumana boemo.

Mekhatlo e latelang e fana ka leseli le eketsehileng ka KTS:

• Sehlopha sa Tšehetso sa Klippel-Trenaunay Syndrome - k-t.org
• Motheo oa Matšoao a Tsoalo ea Vascular - www.birthmark.org

Batho ba bangata ba nang le KTS ba sebetsa hantle, leha boemo bona bo ka ama chebahalo ea bona. Batho ba bang ba na le mathata a kelello ho tsoa boemong boo.

Ka linako tse ling ho ka ba le methapo ea mali e sa tloaelehang ka mpeng, e ka hlokang ho hlahlojoa.

Lefu la Klippel-Trenaunay-Weber; KTS; Angio-osteohypertrophy; Li-hypertrophicans tsa Hemangiectasia; Li-verucosus hypertrophicans; Capillary-lymphatico-venous malformation (CLVM)

Greene AK, Mulliken JB. Liphoso tsa vascular. Ka: Rodriguez ED, Losee JE, Neligan PC, eds. Ho Buuoa ka polasetiki: Buka ea 3: Ho Buuoa ha Craniofacial, Hlooho le Nko le Phekolo ea Bana ea Pulasetiki. La 4 ed. Philadelphia, PA: Elsevier; 2018: khaolo ea 39.

KT webosaete ea Sehlopha sa Ts'ehetso. Litataiso tsa litloaelo tsa bongaka tsa Klippel-Trenaunaysyndrome (KTS). k-t.org/assets/images/content/BCH-Klippel-Trenaunay-Syndrome-Management-Guidelines-1-6-2016.pdf. E ntlafalitsoe ka la 6 Pherekhong 2016. E fihlile ka la 5 Pulungoana, 2019.

Longman RE. Lefu la Klippel-Trenaunay-Weber. Ka: Copel JA, D'Alton ME, Feltovich H, et al, bahlophisi. Ho Nahana ka Thibelo. Lekhetlo la bobeli. Philadelphia, PA: Elsevier; 2018: khaolo ea 131.

McCormick AA, Grundwaldt LJ. Liphoso tsa vascular. Ka: Zitelli BJ, McIntire SC, Nowalk AJ, li-eds. Zitelli le Davis ’Atlas of Pediatric Physical Diagnosis. La 7th. Philadelphia, PA: Elsevier; 2018: khaolo ea 10.