Ntlha ea tlhahlobo ea IX

Ntho ea IX assay ke teko ea mali e lekanyang ts'ebetso ea factor IX. Ena ke e 'ngoe ea liprotheine tse' meleng tse thusang mali ho koala.

Ho hlokahala sampole ea mali.

U kanna ua hloka ho emisa ho noa meriana pele ho tlhahlobo ena. Mofani oa hao oa tlhokomelo ea bophelo o tla u joetsa hore na ke life.

Ha nale e kentsoe ho hula mali, batho ba bang ba utloa bohloko bo itekanetseng. Ba bang ba ikutloa feela ho hlaba kapa ho hlaba. Kamora moo, ho kanna ha ba le ho longoa kapa ho longoa hanyenyane. Haufinyane sena sea fela.

Teko ena e sebelisetsoa ho fumana sesosa sa ho tsoa mali haholo (ho fokotseha hoa mali). Kapa, ​​ho ka laeloa haeba setho sa lelapa se tsejoa hore se na le haemophilia B. Teko e kanna ea etsoa ho bona hore na kalafo ea haemophilia B e sebetsa hantle hakae.

Boleng bo tloaelehileng ke 50% ho isa ho 200% ea taolo ea laboratori kapa boleng ba tšupiso.

Mekhahlelo e tloaelehileng ea boleng e ka fapana hanyane hara lilaboratori tse fapaneng. Labs tse ling li sebelisa litekanyo tse fapaneng kapa li kanna tsa leka mehlala e fapaneng. Bua le mofani oa hau ka moelelo oa sephetho sa hau sa liteko.

Mehlala e kaholimo e bonts'a litekanyo tse tloaelehileng bakeng sa liphetho bakeng sa liteko tsena.

Ho fokotseha ha tšebetso ea IX ho ka amana le:

• Hemophilia B (boloetse bo tsoang mali bo bakoang ke khaello ea mali a koalang mali IX)
• Ho hloka taolo moo liprotheine tse laolang ho hoama ha mali li bang matla ho feta (li fetisitsoeng ka har'a intravascular coagulation)
• Fat malabsorption (e sa monye mafura a lekaneng lijong tsa hau)
• Lefu la sebete (joalo ka cirrhosis)
• Khaello ea Vitamin K
• Ho nka litšila tsa mali

Ha ho na kotsi e kholo ea ho nkuoa mali a hau. Methapo le methapo li fapana ka boholo ho tloha ho motho e mong ho ea ho o mong, le ho tloha lehlakoreng le leng la 'mele ho ea ho le leng. Ho fumana sampole ea mali ho batho ba bang ho ka ba thata ho feta ho ba bang.

Likotsi tse ling tse amanang le ho huloa mali li nyane, empa li ka kenyelletsa:

• Ho tsoa mali a mangata
• Ho akheha kapa ho ikutloa o le hlooho e boima
• Li-punctures tse ngata ho fumana methapo
• Hematoma (mali a bokellanang ka tlasa letlalo)
• Tšoaetso (kotsi e nyane neng kapa neng ha letlalo le robehile)

Hangata tlhahlobo ena e etsoa ho batho ba nang le mathata a ho tsoa mali. Kotsi ea ho tsoa mali a mangata e batla e feta ea batho ba se nang mathata a ho tsoa mali.

Teko ea Keresemese; Serum factor IX; Hemophilic factor B; Karolo ea Plasma thromboplastin; PTC

Carcao M, Moorehead P, Lillicrap D.Hemophilia A le B. Ho: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Melao-motheo le Tloaelo ea Motheo. La 7th. Philadelphia, PA: Elsevier; 2018: khaolo ea 135.

CC ea Chernecky, Berger BJ. Ntlha ea IX (Ntlha ea Keresemese, hemophilic factor B, karolo ea plasma thromboplastin, PTC) - mali. Ka: Chernecky CC, Berger BJ, bahlophisi. Liteko tsa Laboraro le Mekhoa ea Tlhatlhobo. La 6th. St Louis, MO: Elsevier Saunders; 2013: 505-506.

Tlhahlobo ea laboratori ea mathata a hemostatic le thrombotic. Ka: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Melao-motheo le Tloaelo ea Motheo. La 7th. Philadelphia, PA: Elsevier; 2018: khaolo ea 129.