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Recent Advances in the Pharmacologic Management of Idiopathic Hypersomnia
Video: Recent Advances in the Pharmacologic Management of Idiopathic Hypersomnia

Idiopathic hypersomnia (IH) ke lefu la ho robala leo ho lona motho a robalang haholo (hypersomnia) motšehare mme a na le bothata bo boholo ba ho tsosoa borokong. Idiopathic e bolela hore ha ho na lebaka le hlakileng.

IH e tšoana le ho tšoaroa ke lefu la ho robala ka lehare hobane u otsela haholo. E fapane le narcolepsy hobane IH ha hangata e kenyelletsa ho robala ka tšohanyetso (litlhaselo tsa boroko) kapa ho lahleheloa ke taolo ea mesifa ka lebaka la maikutlo a matla (cataplexy). Hape, ho fapana le narcolepsy, ho robala ha IH hangata ha ho khatholle.

Hangata matšoao a hlaha butle ha a le lilemong tsa bocha kapa bocheng. Li kenyeletsa:

  • Ho robala motšehare ho sa imollang ho otsela
  • Bothata ba ho tsoha borokong bo bolelele - bo ka ikutloa bo ferekane kapa bo ferekane ('' botahoa ba boroko '')
  • Tlhoko e eketsehileng ea ho robala motšehare - leha o le mosebetsing, kapa nakong ea lijo kapa moqoqo
  • Nako e eketsehileng ea ho robala - ho fihlela lihora tse 14 ho isa ho tse 18 ka letsatsi

Matšoao a mang a kenyeletsa:

  • Ho tšoenyeha
  • Ho ikutloa u tenehile
  • Ho felloa ke takatso ea lijo
  • Matla a tlase
  • Ho se phomole
  • Butle monahano kapa puo
  • Ho ba le bothata ba ho hopola

Mofani oa tlhokomelo ea bophelo o tla botsa ka nalane ea hau ea boroko. Mokhoa o tloaelehileng ke ho nahana ka lisosa tse ling tse ka bakang boroko bo feteletseng ba motšehare.


Mathata a mang a boroko a ka bakang boroko ba motšehare a kenyelletsa:

  • Bokhachane
  • Ho thibela ho koaleha moea ka nakoana borokong
  • Boloetse ba leoto bo se nang phomolo

Lisosa tse ling tsa boroko bo fetelletseng li kenyelletsa:

  • Ho tepella maikutlo
  • Meriana e itseng
  • Ts'ebeliso ea lithethefatsi le joala
  • Ts'ebetso e tlase ea qoqotho
  • Kotsi e fetileng ea hlooho

Liteko tse ka laeloang li kenyelletsa:

  • Teko ea latency ea boroko bo bongata (teko ea ho bona hore na ho nka nako e kae ho robala nakong ea boroko motšehare)
  • Ho ithuta boroko (polysomnography, ho khetholla mathata a mang a boroko)

Ho ka etsoa liteko tsa bophelo bo botle ba kelello bakeng sa khatello ea maikutlo.

Mofani oa hau o tla fana ka meriana e hlasimollang e kang amphetamine, methylphenidate, kapa modafinil. Litlhare tsena li kanna tsa se sebetse hantle bakeng sa boemo bona joalo ka ha li etsa bakeng sa boroko.

Liphetoho tsa bophelo tse ka thusang ho kokobetsa matšoao le ho thibela kotsi li kenyelletsa:

  • Qoba joala le meriana e ka mpefatsang boemo
  • Qoba ho sebelisa makoloi kapa ho sebelisa lisebelisoa tse kotsi
  • Qoba ho sebetsa bosiu kapa mesebetsing ea boithabiso e liehang ho robala

Buisana le mofani oa hau ka boemo ba hau haeba u pheta linako tsa boroko mots'eare. Li kanna tsa ba ka lebaka la bothata ba bongaka bo hlokang ho etsoa liteko tse ling.


Hypersomnia - idiopathic; Ho otsela - idiopathic; Somnolence - idiopathic

  • Mekhoa ea boroko ho bacha le ba tsofetseng

Billiard M, Sonka K. Idiopathic hypersomnia. Robala Med Rev. 2016; 29: 23-33. PMID: 26599679 www.ncbi.nlm.nih.gov/pubmed/26599679.

Dauvilliers Y, Bassetti CL. Idiopathic hypersomnia. Ka: Kryger M, Roth T, Dement WC, bahlophisi. Melao-motheo le Tloaelo ea Meriana ea Boroko. La 6th. Philadelphia, PA: Elsevier; 2017: khaolo ea 91.

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