Sengoli: William Ramirez
Letsatsi La Creation: 24 September 2021
Ntlafatsa Letsatsi: 1 Phupu 2024
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12.Clinical Live Teaching : Hereditary Motor Sensory Neuropathy
Video: 12.Clinical Live Teaching : Hereditary Motor Sensory Neuropathy

Sensorimotor polyneuropathy ke boemo bo bakang ho fokotseha ha bokhoni ba ho sisinyeha kapa ho ikutloa (sensation) ka lebaka la tšenyo ea methapo.

Neuropathy e bolela lefu la, kapa tšenyo ea methapo. Ha e hlaha kantle ho sistimi e bohareng ea methapo (CNS), ke hore, boko le lesapo la mokokotlo, e bitsoa peripheral neuropathy. Mononeuropathy e bolela hore ho ameha methapo e le 'ngoe. Polyneuropathy e bolela hore methapo e mengata e likarolong tse fapaneng tsa 'mele ea ameha.

Neuropathy e ka ama methapo e fanang ka maikutlo (methapo ea kutlo ea kutlo) kapa ea baka motsamao (motor neuropathy). E ka boela ea ama bobeli, moo ho ka thoeng e bitsoa sensorimotor neuropathy.

Sensorimotor polyneuropathy ke ts'ebetso ea 'mele (systemic) e senyang lisele tsa methapo, methapo ea methapo (li-axon) le masira a koahelang methapo (myelin sheath). Tšenyo ea sekoaelo sa sele ea methapo e etsa hore matšoao a methapo a fokotsehe kapa a emise. Tšenyo ea fiber ea methapo kapa sele eohle ea methapo e ka etsa hore methapo e emise ho sebetsa. Tse ling tsa methapo ea kutlo li hlaha ho feta lilemo, ha tse ling li ka qala le ho ba matla nakong ea matsatsi le matsatsi.


Tšenyo ea methapo e ka bakoa ke:

  • Ho itšireletsa mafung (ha 'mele o itlhasela) mathata
  • Maemo a hatellang methapo
  • Phokotso ea phallo ea mali ho ea methapong
  • Maloetse a senyang sekhomaretsi (lisele tse hokahanyang) tse ts'oereng lisele le lisele
  • Ho ruruha (ho ruruha) ha methapo

Maloetse a mang a lebisa ho polyneuropathy eo haholo-holo e utloang kapa haholo-holo makoloi. Lisosa tse ka bang teng tsa sensorimotor polyneuropathy li kenyelletsa:

  • Ho lemalla ho noa joala
  • Ponahalo ea polyneuropathy ea Amyloid
  • Mathata a ho itšireletsa mafung, joalo ka Sjögren syndrome
  • Kankere (e bitsoang paraneoplastic neuropathy)
  • Nako e telele (e sa foleng) ho ruruha ha pelo
  • Lefu la lefu la tsoekere
  • Phekolo ea methapo e amanang le lithethefatsi, ho kenyeletsoa chemotherapy
  • Lefu la Guillain-Barré
  • Lefu la neuropathy
  • HIV / AIDS
  • Tšoelesa e tlaase
  • Lefu la Parkinson
  • Khaello ea vithamine (livithamini B12, B1, le E)
  • Tšoaetso ea kokoana-hloko ea Zika

Matšoao a ka kenyelletsa efe kapa efe ea tse latelang:


  • Ho fokotseha ha maikutlo sebakeng sefe kapa sefe sa 'mele
  • Ho ba thata ho koenya kapa ho hema
  • Ho thata ho sebelisa matsoho kapa matsoho
  • Ho thata ho sebelisa maoto kapa maoto
  • Ho thata ho tsamaea
  • Bohloko, ho chesa, ho hlohlona, ​​kapa maikutlo a sa tloaelehang sebakeng sefe kapa sefe sa 'mele (se bitsoang neuralgia)
  • Bofokoli ba sefahleho, matsoho kapa maoto, kapa karolo efe kapa efe ea 'mele
  • Ho oa ka linako tse ling ka lebaka la ho hloka botsitso le ho se utloe mobu tlasa maoto a hau

Matšoao a ka hlaha kapele (joalo ka Guillain-Barré syndrome) kapa butle butle ho feta libeke ho isa ho lilemo. Hangata matšoao a hlaha mahlakore ka bobeli a 'mele. Hangata, li qala lipheletsong tsa menoana ea maoto pele.

Mofani oa tlhokomelo ea bophelo o tla u hlahloba le ho botsa matšoao a hau. Tlhahlobo e ka bonts'a:

  • Ho fokotseha ha maikutlo (ho ka ama ho ama, bohloko, ho thothomela kapa boemo ba maikutlo)
  • Maikutlo a fokotsehileng (hangata maqaqailana)
  • Ho fokola ha mesifa
  • Mesifa e sotheha
  • Bofokoli ba mesifa
  • Ho shoa litho

Liteko li ka kenyelletsa:


  • Biopsy ea methapo e amehileng
  • Liteko tsa mali
  • Teko ea motlakase ea mesifa (EMG)
  • Teko ea motlakase ea tsamaiso ea methapo
  • X-ray kapa liteko tse ling tsa ho nka litšoantšo, joalo ka MRI

Lipheo tsa kalafo li kenyelletsa:

  • Ho fumana sesosa
  • Ho laola matšoao
  • Ho khothaletsa boithati ba motho le boikemelo

Ho latela lebaka, kalafo e ka kenyelletsa:

  • Ho fetola meriana, haeba e baka bothata
  • Ho laola boemo ba tsoekere maling, ha lefu la methapo le tsoa ho lefu la tsoekere
  • Ho se noe joala
  • Ho noa limatlafatsi tsa letsatsi le letsatsi tsa phepo e nepahetseng
  • Meriana ea ho sebetsana le sesosa sa polyneuropathy

HO KHothaletsa Boithati le Boikemelo

  • Ho ikoetlisa le ho ikoetlisa ho eketsa ts'ebetso ea methapo e senyehileng
  • Phekolo ea Jobo (ea mosebetsi oa matsoho)
  • Phekolo ea mosebetsing
  • Kalafo ea masapo
  • Phekolo ea 'mele
  • Likoloeana, litšehetso, kapa likotoana

TAOLO MATSOSO

Polokeho e bohlokoa ho batho ba nang le lefu la methapo. Ho hloka taolo ea mesifa le ho fokotseha ha maikutlo ho ka eketsa menyetla ea ho oa kapa likotsi tse ling.

Haeba u na le mathata a ho tsamaea, mehato ena e ka u thusa ho u boloka u sireletsehile:

  • Tlohela mabone a bonesitsoe.
  • Tlosa litšitiso (joalo ka limmete tse hlephileng tse ka thellang fatše).
  • Lekola mocheso oa metsi pele o hlapa.
  • Sebelisa literene.
  • Roala lieta tse sireletsang (joalo ka tse nang le menoana e koetsoeng le lieta tse tlaase).
  • Apara lieta tse nang le bohato bo sa thelleng.

Malebela a mang a kenyelletsa:

  • Lekola maoto a hau (kapa sebaka se seng se amehileng) letsatsi le letsatsi bakeng sa matetetso, libaka tse bulehileng tsa letlalo, kapa likotsi tse ling, tseo u ka 'nang ua se ke oa li bona' me tsa u tšoaetsa.
  • Hlahloba bokahare ba lieta khafetsa bakeng sa matetetso kapa mabala a ka u lematsang maoto.
  • Etela ngaka ea maoto (ngaka ea maoto) ho lekola le ho fokotsa menyetla ea ho lemala maotong a hau.
  • Qoba ho its'etleha ka litsoeng, ho tšela mangole, kapa ho ba maemong a mang a fanang ka khatello e telele libakeng tse ling tsa 'mele.

Meriana e sebelisetsoang ho phekola boemo bona:

  • Ho kokobetsa bohloko bo holimo-le-thekeng le ba ngaka ho fokotsa bohloko ba ho hlaba (neuralgia)
  • Li-anticonvulsants kapa li-anti-depressing
  • Litlolo, litlolo, kapa litlama tse nang le meriana

Sebelisa moriana oa bohloko ha ho hlokahala. Ho boloka 'mele oa hau o le maemong a nepahetseng kapa ho boloka masela a bethe karolong ea' mele e bonolo ho ka thusa ho laola bohloko.

Lihlopha tsena li ka fana ka tlhaiso-leseling e batsi ka lefu la methapo.

  • Motheo oa ts'ebetso ea Neuropathy - www.neuropathyaction.org
  • Motheo oa Pheripherial Neuropathy - www.foundationforpn.org

Maemong a mang, o ka fola ka botlalo ho tsoa pheriferale ea methapo haeba mofani oa hau a ka fumana sesosa mme a se phekola ka katleho, mme haeba tšenyo e sa ame sele ea methapo eohle.

Palo ea bokooa e fapana. Batho ba bang ha ba na bokooa. Ba bang ba lahlehetsoe ke motsamao, ts'ebetso, kapa maikutlo. Mahlaba a methapo a ka ba a sa phutholoha mme a ka nka nako e telele.

Maemong a mang, sensorimotor polyneuropathy e baka matšoao a matla, a sokelang bophelo.

Mathata a ka hlahang a kenyelletsa:

  • Ho holofala
  • Ho tsoa likotsi maotong (ho bakoa ke lieta tse mpe kapa metsi a chesang ha u kena ka bateng)
  • Boikitlaetso
  • Bohloko
  • Ho tsamaea ka thata
  • Bofokoli
  • Ho phefumoloha ho thata kapa ho koenya (maemong a boima)
  • Ho oa ka lebaka la ho hloka botsitso

Bitsa mofani oa hau haeba u lahlehetsoe ke ho sisinyeha kapa ho ikutloa karolong e 'ngoe ea' mele oa hau. Tlhahlobo ea pele le kalafo li eketsa menyetla ea ho laola matšoao.

Polyneuropathy - senotlolo sa kutlo

  • Sisteme ea methapo e bohareng le methapo ea methapo
  • Tsamaiso ea methapo

Craig A, Richardson JK, Ayyangar R. Ntlafatso ea bakuli ba nang le lefu la methapo. Ka: Cifu DX, ed. Phekolo ea 'mele ea Braddom le Tlhabollo. La 5th. Philadelphia, PA: Elsevier; 2016: khaolo ea 41.

Endrizzi SA, Rathmell JP, Hurley RW. Mahlaba a bohloko a methapo ea kutlo. Ka: Benzon HT, Raja SN, Liu SS, Fishman SM, Cohen SP, eds. Bohlokoa ba Meriana ea Bohloko. La 4 ed. Philadelphia, PA: Elsevier; 2018: khaolo ea 32.

Katitji B. Mathata a methapo ea kutlo. Ka: Daroff RB, Jankovic J, Mazziotta JC, Pomeroy SL, bahlophisi. Neurology ea Bradley ho Tloaelo ea Bongaka. La 7th. Philadelphia, PA: Elsevier; 2016: khaolo ea 107.

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