Sengoli: Clyde Lopez
Letsatsi La Creation: 21 Phupu 2021
Ntlafatsa Letsatsi: 23 Phuptjane 2024
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Retroperitoneal fibrosis
Video: Retroperitoneal fibrosis

Retroperitoneal fibrosis ke boloetse bo sa tloaelehang bo thibelang li-tubes (ureters) tse tsamaisang moroto ho tloha liphio ho ea senya.

Retroperitoneal fibrosis e hlaha ha mefuta e meng ea masela a likhoele e le teng kamora mpa le mala. Lisele li theha boima (kapa bongata) kapa lisele tse thata tsa fibrotic. E ka thibela li-tubes tse tsamaisang moroto ho tloha liphio ho ea senya.

Lebaka la bothata bona ha le tsejoe hangata. E atile haholo bathong ba lilemo li 40 ho isa ho tse 60. Banna ba na le menyetla e imenneng habeli ea ho ba le boemo boo joaloka basali.

Matšoao a pele:

  • Bohloko bo bohloko ka mpeng bo eketsehang ka nako
  • Bohloko le phetoho ea 'mala maotong (ka lebaka la phallo ea mali e fokotsehileng)
  • Ho ruruha ha leoto le le leng

Matšoao a morao-rao:

  • Ho fokotsa tlhahiso ea moroto
  • Ha ho na tlhahiso ea moroto (anuria)
  • Ho nyekeloa ke pelo, ho hlatsa, ho fetoha hoa boemo ba kelello ho bakoang ke ho hloleha ha liphio le ho aha lik'hemik'hale tse chefo maling
  • Mahlaba a bohloko ka mpeng le mali setulong (ka lebaka la lefu la lisele tsa mala)

Sesebelisoa sa mpa sa CT ke tsela e molemohali ea ho fumana boima ba retroperitoneal.


Liteko tse ling tse ka thusang ho fumana boemo bona li kenyelletsa:

  • BUN le liteko tsa mali tsa creatinine
  • Intravenous pyelogram (IVP), eseng joalo ka ha e sebelisoa hangata
  • Liphio tsa ultrasound
  • MRI ea mpa
  • Tlhatlhobo ea CAT ea mpa le retroperitoneum

Ho ka boela ha etsoa biopsy ea boima ho felisa mofetše.

Li-corticosteroids li lekoa pele. Bafani ba bang ba tlhokomelo ea bophelo le bona ba fana ka sethethefatsi se bitsoang tamoxifen.

Haeba kalafo ea corticosteroid e sa sebetse, biopsy e lokela ho etsoa ho netefatsa tlhahlobo. Ho ka laeloa meriana e meng ho hatella sesole sa 'mele.

Ha moriana o sa sebetse, ho hlokahala opereishene le lisente (ho hula methapo).

Ponahalo e tla latela boholo ba bothata le boholo ba tšenyo ea liphio.

Tšenyo ea liphio e kanna ea ba ea nakoana kapa ea ka mehla.

Boloetse bona bo ka lebisa ho:

  • Thibelo e tsoelang pele ea methapo e tsoang liphio lehlakoreng le leng kapa ka mahlakore ka bobeli
  • Ho hloleha ha liphio ho sa foleng

Bitsa mofani oa hau haeba u e-na le bohloko bo ka mpeng kapa lehlakore le tlase ha u tsoa moroto.


Leka ho qoba tšebeliso ea nako e telele ea meriana e nang le methysergide. Meriana ena e bontšitsoe e baka retroperitoneal fibrosis. Ka linako tse ling Methysergide e sebelisoa ho phekola hlooho ea migraine.

Idiopathic retroperitoneal fibrosis; Lefu la Ormond

  • Tsamaiso ea monna ea ho ntša metsi

Comperat E, Bonsib SM, Cheng L. Renal pelvis le ureter. Ka: Cheng L, MacLennan GT, Bostwick DG, bahlophisi. Pathology ea ho Buoa ea Urologic. La 4 ed. Philadelphia, PA: Elsevier; 2020: khaolo ea 3.

Nakada SY, Molemo ka ho fetisisa SL. Tsamaiso ea tšitiso e kaholimo ea mosese. Ka: Wein AJ, Kavoussi LR, Partin AW, Peters, CA, bahlophisi. Urology ea Campbell-Walsh. 11th ed. Philadelphia, PA: Elsevier; 2016: khaolo ea 49.

O'Connor OJ, Maher MM. Karolo ea ho ntša metsi: kakaretso ea anatomy, mekhoa le litaba tsa radiation. Ka: Adam A, Dixon AK, Gillard JH, Schaefer-Prokop CM, bahlophisi. Grainger & Allison’s Diagnostic Radiology: Buka ea Litšoantšo ea Bongaka ea Bongaka. La 6th. Philadelphia, PA: Elsevier Churchill Livingstone; 2015: khaolo ea 35.


Shanmugam VK. Vasculitis le li-arteriopathies tse ling tse sa tloaelehang. Ka: Sidawy AN, Perler BA, bahlophisi. Rutherford's Vasculry and Endovascular Therapy. La 9th. Philadelphia, PA: Elsevier; 2019: khaolo ea 137.

Phetoho RH, Mizell J, Badgwell B. Lerako la mpa, umbilicus, peritoneum, mesenteries, omentum le retroperitoneum. Ka: Townsend CM Jr, Beauchamp RD, Evers BM, Mattox KL, eds. Buka ea Sabiston ea Ngaka ea ho Buoa. 20th, ed. Philadelphia, PA: Elsevier Saunders; 2017: khaolo ea 43.

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