Fasciitis ea mahlo

Eosinophilic fasciitis (EF) ke lefu leo ​​ho lona lisele tse ka tlas'a letlalo le ka holim'a mesifa li bitsoang fascia, li ruruhang, li ruruhang le ho ba tenya. Letlalo le matsohong, maotong, molaleng, mpeng kapa maotong le ka ruruha kapele. Boemo bo sa tloaelehang haholo.

EF e kanna ea shebahala e ts'oana le scleroderma, empa ha e amane. Ho fapana le scleroderma, ho EF, menoana ha e amehe.

Lebaka la EF ha le tsejoe. Maemong a mangata a etsahetse kamora ho nka L-tryptophan supplements. Ho batho ba nang le boemo bona, lisele tse tšoeu tsa mali, tse bitsoang li-eosinophil, li aha ka har'a mesifa le lisele. Li-eosinophil li hokahane le khatello ea maikutlo. Lefu lena le atile haholo bathong ba lilemo li 30 ho isa ho 60.

Matšoao a ka kenyelletsa:

• Bonolo le ho ruruha ha letlalo matsohong, maotong, kapa ka linako tse ling manonyello (hangata mahlakore ka bobeli a 'mele)
• Ramatiki
• Lefu la Carpal tunnel
• Bohloko ba mesifa
• Letlalo le lenyane le shebahalang le kakatetse

Liteko tse ka etsoang li kenyelletsa:

• CBC ka phapang
• Gamma globulins (mofuta oa protheine ea sesole sa 'mele)
• Sekhahla sa sedimentation sa Erythrocyte (ESR)
• MRI
• Biopsy ea mesifa
• Letlalo biopsy (biopsy e hloka ho kenyelletsa lisele tse tebileng tsa fascia)

Corticosteroids le meriana e meng e thibelang boitshireletso ba mmele di sebediswa ho kokobetsa matshwao a ho kula. Meriana ena e sebetsa hantle ha e qala kapele ho lefu lena. Lithethefatsi tse seng khahlanong le ho ruruha (li-NSAID) le tsona li ka thusa ho fokotsa matšoao.

Maemong a mangata, boemo bo a fela pele ho lilemo tse 1 ho isa ho tse tharo. Leha ho le joalo, matšoao a ka nka nako e teletsana kapa a khutla.

Ramatiki ke bothata bo sa tloaelehang ba EF. Batho ba bang ba ka ba le mathata a tebileng a mali kapa mofetše o amanang le mali, joalo ka aplastic anemia kapa leukemia. Ponahalo e mpe haholo haeba mafu a mali a hlaha.

Bitsa mofani oa tlhokomelo ea bophelo haeba u na le matšoao a lefu lena.

Ha ho na thibelo e tsebahalang.

Shulman lefu

• Mesifa ea ka ntle e kantle

Aronson JK. Lehlohonolo. E ngotsoe ke: Aronson JK, ed. Litla-morao tsa Meyler tsa Lithethefatsi. 16th ed. Waltham, MA: Elsevier BV ;; 2016: 220-221.

James WD, Elston DM, Tšoara JR, Rosenbach MA, Neuhaus IM. Matšoao a amanang a lisele. Ka: James WD, Elston DM, Tšoara JR, Rosenbach MA, Neuhaus IM, eds. Andrews ’Maloetse a Letlalo: Clinical Dermatology. 13th ed. Philadelphia, PA: Elsevier; 2020: khaolo ea 8.

Lee LA, Werth VP. Letlalo le mafu a rheumatic. Ka: Firestein GS, Budd RC, Gabriel SE, McInnes IB, O'Dell JR, bahlophisi. Kelley le Firestein's Bookbook ea Rheumatology. 10th ed. Philadelphia, PA: Elsevier; 2017: khaolo ea 43.

Pinal-Fernandez I, Selva-O 'Callaghan A, Grau JM. Ho lemoha le ho khetholla li-eosinophilic fasciitis. Iketsetse Auto Rev. 2014; 13 (4-5): 379-382. PMID: 24424187 www.ncbi.nlm.nih.gov/pubmed/24424187.

Mokhatlo oa Naha oa Mathata a Rare. Fasciitis ea mahlo. rarediseases.org/rare-diseases/eosinophilic-fasciitis/. E ntlafalitsoe ka 2016. E fihlile ka la 6 Hlakubele 2017.