Maloetse a tšoaetsanoang ke veno

Pulmonary veno-occlusive lefu (PVOD) ke lefu le sa tloaelehang haholo. E lebisa khatello e phahameng ea mali methapong ea matšoafo (pulmonary hypertension).

Maemong a mangata, sesosa sa PVOD ha se tsejoe. Khatello ea mali e phahameng e hlaha methapong ea methapo. Methapo ena ea matšoafo e hokahane ka kotloloho le lehlakoreng le letona la pelo.

Boemo bo kanna ba amana le tšoaetso ea vaerase. E kanna ea hlaha e le qaka ea mafu a mang a kang lupus, kapa phetisetso ea moko oa masapo.

Boloetse bona bo atile haholo baneng le ho batho ba baholo. Ha lefu lena le ntse le mpefala, le baka:

• Metsu e fokotsitsoeng ea methapo
• Ts'oaetso ea methapo ea methapo
• Ho tiisa le ho ruruha ha matšoafo

Lisosa tse ka bang kotsing ea PVOD li kenyelletsa:

• Nalane ea lelapa ea boemo bona
• Ho tsuba
• Ho hlahisa lintho tse kang trichlorethylene kapa chemotherapy meriana
• Systemic sclerosis (lefu la letlalo le ikemetseng)

Matšoao a ka kenyelletsa efe kapa efe ea tse latelang:

• Phefumoloho e khutšoanyane
• Khohlela e ommeng
• Mokhathala ka boikitlaetso
• Ho akheha
• Ho kgohlela madi
• Ho phefumoloha ho thata ha o rapaletse

Mofani oa tlhokomelo ea bophelo o tla u hlahloba ebe o botsa nalane ea hau ea bongaka le matšoao a hau.

Tlhahlobo e ka senola:

• Khatello e eketsehileng methapong ea molala
• Ho ts'oarana ha menoana
• Mmala o moputsoa oa letlalo ka lebaka la khaello ea oksijene (cyanosis)
• Ho ruruha maotong

Mofani oa hau a ka utloa melumo e sa tloaelehang ea pelo ha a mametse sefuba le matšoafo ka stethoscope.

Liteko tse latelang li ka etsoa:

• Likhase tsa mali tse ngata
• Oximetry ea mali
• X-ray sefubeng
• Sefuba CT
• Catheterization ea pelo
• Liteko tsa mosebetsi oa matšoafo
• Echocardiogram
• Biopsy ea matšoafo

Hajoale ha ho na kalafo e tsebahalang e sebetsang. Leha ho le joalo, meriana e latelang e ka thusa batho ba bang:

• Meriana e atisang methapo ea mali (vasodilators)
• Meriana e laolang boits'ireletso ba sesole sa 'mele (joalo ka azathioprine kapa steroids)

Ho kenyelletsa phepelo ea matšoafo ho ka hlokahala.

Phello hangata e futsanehile haholo ho masea, ka sekhahla sa pholoho sa libeke tse 'maloa feela. Ho pholoha ho batho ba baholo e ka ba likhoeli ho isa ho lilemo tse 'maloa.

Mathata a PVOD a ka kenyelletsa:

• Ho phefumoloha ho thata ho mpefala, ho kenyelletsa le bosiu (ho koaleha moea ka nakoana borokong)
• Matšoafo a khatello ea mali
• Ho hloleha ha pelo ka lehlakoreng le letona (cor pulmonale)

Bitsa mofani oa hau haeba u na le matšoao a lefu lena.

Maloetse a amanang le lefu la vaso

• Tsamaiso ea phefumoloho

Chin K, Channick RN. Matšoafo a khatello ea mali. Ka: Broaddus VC, Mason RJ, Ernst JD, et al, li-eds. Buka ea Bongaka ea Phefumoloho ea Murray le Nadel. La 6th.Philadelphia, PA: Elsevier Saunders; 2016: khaolo ea 58.

Churg A, Wright JL. Matšoafo a khatello ea mali. Ka: Leslie KO, Wick MR, bahlophisi. Mokhoa o sebetsang oa Pulmonary Pathology: Mokhoa oa ho Itlhahloba. 3rd ed. Philadelphia, PA: Elsevier; 2018: khaolo ea 12.

Mclaughlin VV, Humbert M. Pulmonary khatello ea meriana. Ka: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. Lefu la pelo la Braunwald: Buka ea bongaka ea meriana ea pelo. 11th ed. Philadelphia, PA: Elsevier; 2019: khaolo ea 85.